CLASSIFICATION OF DISEASES AND INJURIES I. INFECTIOUS AND PARASITIC DISEASES (001-139) Includes: diseases generally recognized as communicable or transmissible as well as a few diseases of unknown but possibly infectious origin Excludes: acute respiratory infections (460-466) influenza (487.-) certain localized infections Note: Categories for "late effects" of infectious and parasitic diseases are to be found at 137.- to 139.- INTESTINAL INFECTIOUS DISEASES (001-009) Excludes: helminthiases (120-129) 001 Cholera 001.0 Due to Vibrio cholerae 001.1 Due to Vibrio cholerae el tor 001.9 Unspecified 002 Typhoid and paratyphoid fevers 002.0 Typhoid fever Typhoid (fever) (infection) [any site] 002.1 Paratyphoid fever A 002.2 Paratyphoid fever B 002.3 Paratyphoid fever C 002.9 Paratyphoid fever, unspecified 003 Other salmonella infections Includes: infection or food poisoning by Salmonella [any serotype] 003.0 Salmonella gastroenteritis Salmonellosis 003.1 Salmonella septicaemia 003.2 Localized salmonella infections Salmonella: Salmonella: arthritis osteomyelitis meningitis pneumonia 003.8 Other 003.9 Unspecified Salmonella infection NOS 004 Shigellosis Includes: bacillary dysentery 004.0 Shigella dysenteriae Infection by group A Shigella (Schmitz) (Shiga) 004.1 Shigella flexneri Infection by group B Shigella 004.2 Shigella boydii Infection by group C Shigella 004.3 Shigella sonnei Infection by group D Shigella 004.8 Other 004.9 Unspecified 005 Other food poisoning (bacterial) Excludes: salmonella infections (003.-) toxic effect of noxious foodstuffs (988.-) 005.0 Staphylococcal food poisoning Staphylococcal toxaemia specified as due to food 005.1 Botulism Food poisoning due to Clostridium botulinum 005.2 Food poisoning due to Clostridium perfringens [Cl. welchii] Enteritis necroticans 005.3 Food poisoning due to other Clostridia 005.4 Food poisoning due to Vibrio parahaemolyticus 005.8 Other bacterial food poisoning Food poisoning due to Bacillus cereus Excludes: salmonella food poisoning (003.-) 005.9 Food poisoning, unspecified 006 Amoebiasis Includes: infection due to Entamoeba histolytica Excludes: amoebiasis due to organisms other than Entamoeba histolytica (007.8) 006.0 Acute amoebic dysentery without mention of abscess Acute amoebiasis 006.1 Chronic intestinal amoebiasis without mention of abscess Chronic: amoebiasis amoebic dysentery 006.2 Amoebic nondysenteric colitis 006.3 Amoebic liver abscess 006.4 Amoebic lung abscess Amoebic abscess of lung (and liver) 006.5 Amoebic brain abscess Amoebic abscess of brain (and liver) (and lung) 006.6 Amoebic skin ulceration 006.8 Amoebic infection of other sites Amoebic: Amoeboma appendicitis balanitis Excludes: specific infections by free-living amoebae (136.2) 006.9 Amoebiasis, unspecified Amoebiasis NOS 007 Other protozoal intestinal diseases Includes: protozoal: colitis diarrhea dysentery 007.0 Balantidiasis Infection by Balantidium coli 007.1 Giardiasis Infection by Giardia lamblia Lambliasis 007.2 Coccidiosis Infection by Isospora belli and Isospora hominis Isosporosis 007.3 Intestinal trichomoniasis 007.8 Other protozoal intestinal diseases 007.9 Unspecified Flagellate diarrhea Protozoal dysentery NOS 008 Intestinal infections due to other organisms Includes: any terms listed in 009.-with mention of the responsible organisms Excludes: food poisoning by these organisms (005.-) 008.0 Escherichia coli [E. coli] 008.1 Arizona 008.2 Aerobacter aerogenes 008.3 Proteus (mirabilis) (morganii) 008.4 Other specified bacteria Staphylococcal enterocolitis 008.5 Bacterial enteritis, unspecified 008.6 Enteritis due to specified virus Enteritis due to: adenovirus enterovirus 008.8 Other organism, not elsewhere classified Viral: enteritis NOS gastroenteritis Excludes: influenza with involvement of gastrointestinal tract (487.8) 009 Ill-defined intestinal infections Excludes: diarrheal disease due to specified organism (001-008) diarrhea following gastrointestinal surgery (564.4) intestinal malabsorption (579.-) ischaemic enteritis (557.-) other noninfective gastroenteritis and colitis (558) regional enteritis (555.-) ulcerative colitis (556) 009.0 Infectious colitis, enteritis, and gastroenteritis Colitis (septic) Dysentery: Enteritis (septic) NOS Gastroenteritis (septic) catarrhal hemorrhagic 009.2 Infectious diarrhea Diarrhea: dysenteric epidemic Infectious diarrheal disease NOS TUBERCULOSIS (010-018) Includes: infection by Mycobacterium tuberculosis (human) (bovine) Excludes: congenital tuberculosis (771.2) 010 Primary tuberculous infection 010.0 Primary tuberculous complex 010.1 Tuberculous pleurisy in primary progressive tuberculosis 010.8 Other primary progressive tuberculosis Excludes: tuberculous erythema nodosum (017.1) 010.9 Unspecified 011 Pulmonary tuberculosis Use additional code, if desired, to identify any associated silicosis (502) 011.0 Tuberculosis of lung, infiltrative 011.1 Tuberculosis of lung, nodular 011.2 Tuberculosis of lung with cavitation 011.3 Tuberculosis of bronchus Excludes: isolated bronchial tuberculosis (012.2) 011.4 Tuberculous fibrosis of lung 011.5 Tuberculous bronchiectasis 011.6 Tuberculous pneumonia [any form] 011.7 Tuberculous pneumothorax 011.8 Other pulmonary tuberculosis 011.9 Unspecified Respiratory tuberculosis NOS Tuberculosis of lung NOS 012 Other respiratory tuberculosis Excludes: respiratory tuberculosis, unspecified (011.9) 012.0 Tuberculous pleurisy Tuberculosis of pleura Tuberculous empyema Tuberculous hydrothorax Excludes: pleurisy with effusion without mention of cause (511.9) tuberculous pleurisy in primary progressive tuberculosis (010.1) 012.1 Tuberculosis of intrathoracic lymph nodes Tuberculosis of lymph nodes: hilar mediastinal tracheobronchial Excludes: when specified as primary (010.-) 012.2 Isolated tracheal or bronchial tuberculosis 012.3 Tuberculous laryngitis Tuberculosis of glottis 012.8 Other Tuberculosis of: mediastinum nasopharynx nose (septum) sinus [any nasal] 013 Tuberculosis of meninges and central nervous system 013.0 Tuberculous meningitis Tuberculosis of meninges (cerebral) (spinal) Tuberculous: leptomeningitis meningoencephalitis Excludes: tuberculoma of meninges (013.1) 013.1 Tuberculoma of meninges 013.8 Other Tuberculoma } of Tuberculosis } brain Tuberculous: abscess of brain myelitis 013.9 Unspecified Tuberculosis of central nervous system NOS 014 Tuberculosis of intestines, peritoneum, and mesenteric glands Tuberculosis (of): Tuberculous anus ascites intestine (large) (small) enteritis rectum peritonitis retroperitoneal (lymph nodes) 015 Tuberculosis of bones and joints Includes: tuberculous: arthritis necrosis of bone osteitis osteomyelitis synovitis tenosynovitis 015.0 Vertebral column Pott's: Tuberculous: curvature kyphosis disease spondylitis 015.1 Hip 015.2 Knee 015.7 Other bone Tuberculous dactylitis Tuberculous mastoiditis 015.8 Other joint 015.9 Unspecified 016 Tuberculosis of genitourinary system 016.0 Kidney Tuberculous pyelitis Tuberculous pyelonephritis 016.1 Other urinary organs Tuberculosis of bladder Tuberculosis of ureter 016.2 Epididymis 016.3 Other male genital organs Tuberculosis of: prostate seminal vesicle testis 016.4 Female genital organs Tuberculous: oophoritis salpingitis 016.9 Unspecified 017 Tuberculosis of other organs 017.0 Skin and subcutaneous cellular tissue Lupus: Tuberculosis: NOS colliquativa exedens cutis vulgaris lichenoides Scrofuloderma papulonecrotica verrucosa cutis Excludes: lupus erythematosus (695.4) disseminated (710.0) lupus NOS (710.0) 017.1 Erythema nodosum with hypersensitivity reaction in tuberculosis Bazin's disease Erythema: induratum nodosum, tuberculous Tuberculosis indurativa Excludes: erythema nodosum NOS (695.2) 017.2 Peripheral lymph nodes Scrofula Scrofulous abscess Tuberculous adenitis Excludes: tuberculosis of lymph nodes: bronchial and mediastinal (012.1) mesenteric and retroperitoneal (014) tuberculous tracheobronchial adenopathy (012.1) 017.3 Eye Tuberculous: chorioretinitis, disseminated episcleritis interstitial keratitis iridocyclitis, chronic keratoconjunctivitis (phlyctenular) 017.4 Ear Tuberculosis of ear Tuberculous otitis media Excludes: tuberculous mastoiditis (015.7) 017.5 Thyroid gland 017.6 Adrenal glands Addison's disease, tuberculous 017.7 Spleen 017.8 Other Tuberculosis of: endocardium [any valve] esophagus myocardium pericardium 018 Miliary tuberculosis Includes: tuberculosis: disseminated generalized miliary, whether of a single specified site, multiple sites, or unspecified site polyserositis 018.0 Acute 018.8 Other 018.9 Unspecified ZOONOTIC BACTERIAL DISEASES (020-027) 020 Plague Includes: infection by Yersinia pestis 020.0 Bubonic 020.1 Cellulocutaneous 020.2 Septicaemic 020.3 Primary pneumonic 020.4 Secondary pneumonic 020.5 Pneumonic, unspecified 020.8 Other Abortive plague Ambulatory plague Pestis minor 020.9 Unspecified 021 Tularemia Includes: infection by Francisella tularensis Deer fly fever rabbit fever 022 Anthrax 022.0 Cutaneous anthrax Malignant pustule 022.1 Pulmonary anthrax Respiratory anthrax Wool-sorters' disease 022.2 Gastrointestinal anthrax 022.3 Anthrax septicaemia 022.8 Other manifestations 022.9 Unspecified 023 Brucellosis Includes: fever: Malta Mediterranean undulant 023.0 Brucella melitensis 023.1 Brucella abortus 023.2 Brucella suis 023.3 Brucella canis 023.8 Other Infection by more than one organism 023.9 Unspecified 024 Glanders Infection by: Actinobacillus mallei Farcy Malleomyces mallei Malleus Pseudomonas mallei 025 Melioidosis Infection by: Malleomyces pseudomallei Pseudomonas pseudomallei Whitmore's bacillus Pseudoglanders 026 Rat-bite fever 026.0 Spirillary fever Rat-bite fever due to Spirillum minor [S. minus] Sodoku 026.1 Streptobacillary fever Epidemic arthritic erythema Haverhill fever Rat-bite fever due to Streptobacillus moniliformis 026.9 Unspecified 027 Other zoonotic bacterial diseases 027.0 Listeriosis Infection by Listeria monocytogenes Meningitis by Listeria monocytogenes Meningoencephalitis by Listeria monocytogenes Septicaemia by Listeria monocytogenes Excludes: congenital listeriosis (771.2) 027.1 Erysipelothrix infection Erysipeloid (of Rosenbach) Infection by Erysipelothrix insidiosa [E. rhusiopathiae] Septicaemia by Erysipelothrix insidiosa [E. rhusiopathiae] 027.2 Pasteurellosis Pasteurella pseudotuberculosis infection Mesenteric adenitis by Pasteurella multocida [P. septica] Septic infection (cat bite) (dog bite) by Pasteurella multocida [P. septica] Excludes: infection by: Francisella tularensis (021) Yersinia pestis (020.-) 027.8 Other 027.9 Unspecified OTHER BACTERIAL DISEASES (030-041) Excludes: bacterial venereal diseases (098.-, 099.-) bartonellosis (088.0) 030 Leprosy Includes: Hansen's disease Infection by Mycobacterium leprae 030.0 Lepromatous [type L] Lepromatous leprosy (macular) (diffuse) (infiltrated) (nodular) (neuritic) 030.1 Tuberculoid [type T] Tuberculoid leprosy (macular) (maculoanesthetic) (major) (minor) (neuritic) 030.2 Indeterminate [group I] Indeterminate leprosy (macular) (neuritic) 030.3 Borderline [group B] Borderline or dimorphous leprosy (infiltrated) (neuritic) 030.8 Other 030.9 Unspecified 031 Diseases due to other mycobacteria 031.0 Pulmonary Infection by Mycobacterium: avium intracellulare [Battey bacillus] kansasii Battey disease 031.1 Cutaneous Buruli ulcer Infection by Mycobacterium: marinum [M. balnei] ulcerans 031.8 Other 031.9 Unspecified Atypical mycobacterium infection NOS 032 Diphtheria Includes: infection by Corynebacterium diphtheriae 032.0 Faucial diphtheria Membranous angina, diphtheritic 032.1 Nasopharyngeal diphtheria 032.2 Anterior nasal diphtheria 032.3 Laryngeal diphtheria Laryngotracheitis, diphtheritic 032.8 Other Cutaneous diphtheria 032.9 Diphtheria, unspecified 033 Whooping cough 033.0 Bordetella pertussis [B. pertussis] 033.1 Bordetella parapertussis [B. parapertussis] 033.8 Other specified organism 033.9 Whooping cough, unspecified organism 034 Streptococcal sore throat and scarlatina 034.0 Streptococcal sore throat Streptococcal: Septic: angina angina laryngitis sore throat pharyngitis tonsillitis 034.1 Scarlatina Scarlet fever 035 Erysipelas Excludes: postpartum or puerperal erysipelas (670) 036 Meningococcal infection 036.0 Meningococcal meningitis Cerebrospinal fever (meningococcal) Meningitis: cerebrospinal epidemic 036.1 Meningococcal encephalitis 036.2 Meningococcaemia Meningococcal septicaemia 036.3 Waterhouse-Friderichsen syndrome, meningococcal Meningococcal hemorrhagic adrenalitis Meningococcic adrenal syndrome Waterhouse-Friderichsen syndrome NOS 036.4 Meningococcal carditis Meningococcal: endocarditis pericarditis 036.8 Other Meningococcal optic neuritis 036.9 Unspecified Meningococcal infection NOS 037 Tetanus Excludes: tetanus: complicating abortion (634-638 with fourth digit .0, 639.0) complicating ectopic or molar pregnancy (639.0) neonatorum (771.3) puerperal (670) 038 Septicaemia Excludes: during labor (659.3) following ectopic or molar pregnancy (639.0) following infusion, injection, transfusion, or vaccination (999.3) postoperative (998.5) postpartum, puerperal (670) when complicating abortion (634-638 with fourth digit .0, 639.0) 038.0 Streptococcal septicaemia 038.1 Staphylococcal septicaemia 038.2 Pneumococcal septicaemia 038.3 Septicaemia due to anaerobes Excludes: gas gangrene (040.0) anaerobic streptococci (038.0) 038.4 Septicaemia due to other gram-negative organisms Gram-negative septicaemia NOS 038.8 Other specified septicaemias Excludes: septicaemia (due to): anthrax (022.3) gonococcal (098.8) herpetic (054.5) meningococcal (036.2) septicaemic plague (020.2) 038.9 Unspecified septicaemia Septicaemia NOS Excludes: bacteremia NOS (790.7) 039 Actinomycotic infections Includes: actinomycotic mycetoma infection by Actinomycetales such as species of Actinomyces, Actinomadura, Nocardia, Streptomyces maduromycosis (actinomycotic) 039.0 Cutaneous Erythrasma Trichomycosis axillaris 039.1 Pulmonary 039.2 Abdominal 039.3 Cervicofacial 039.4 Madura foot Excludes: madura foot due to mycotic infection (117.4) 039.8 Of other specified sites 039.9 Of unspecified site Actinomycosis NOS Maduromycosis NOS Nocardiosis NOS 040 Other bacterial diseases Excludes: bacteraemia NOS (790.7) bacterial infection NOS (041.9) 040.0 Gas gangrene Gas bacillus infection or gangrene Malignant edema Myositis, clostridial Infection by Clostridium: histolyticum oedematiens perfringens [welchii] septicum sordellii 040.1 Rhinoscleroma 040.2 Whipple's disease Intestinal lipodystrophy 040.3 Necrobacillosis 040.8 Other bacterial diseases Tropical pyomyositis 041 Bacterial infection in conditions classified elsewhere and of unspecified site Note: This category will rarely be used for primary coding. It is provided as an additional code where it is desired to identify the bacterial agent in diseases classified elsewhere. This category will also be used in primary coding to classify bacterial infections of unspecified nature or site. Excludes: bacteraemia NOS (790.7) septicaemia (038.-) 041.0 Streptococcus 041.1 Staphylococcus 041.2 Pneumococcus 041.3 Friedlander's bacillus 041.4 Escherichia coli [E.coli] 041.5 Haemophilus influenzae [H. influenzae] 041.6 Proteus (mirabilis) (morganii) 041.7 Pseudomonas 041.8 Other Aerobacter aerogenes Other cocci, not elsewhere classified Eaton's agent Pleuropneumonia-like organisms [PPLO] Mima polymorpha Mycoplasma 041.9 Bacterial infection, unspecified HUMAN IMMUNODEFICIENCY VIRUS (HIV) INFECTION (042-044) Note: Beginning with data for 1987, the National Center for Health Statistics introduced categories 042-044 for classifying and coding HIV infection. Note: In this classification, the following terms are used to define and to represent other terms that are referable to these categories 042-044. 1. AIDS: Acquired immune deficiency syndrome Acquired immunodeficiency syndrome 2. AIDS-like syndrome: AIDS-like disease (illness) (syndrome) ARC AIDS-related complex Pre-AIDS AIDS-related conditions Prodromal-AIDS 3. HIV infection (disease) (illness) AAV (disease) (illness) (infection) AIDS-associated retrovirus (disease) (illness) (infection) AIDS-associated virus (disease) (illness) (infection) AIDS-related virus (disease) (illness) (infection) AIDS virus (disease) (illness) (infection) ARV (disease) (illness) (infection) Human immunodeficiency virus (disease) (illness) (infection) Human immunovirus (disease) (illness) (infection) Human T-cell lymphotropic virus-III (disease) (illness) (infection) HTLV-III (disease) (illness) (infection) HTLV-III/LAV (disease) (illness) (infection) LAV (disease) (illness) (infection) LAV/HTLV-III (disease) (illness) (infection) Lymphadenopathy-associated virus (disease) (illness) (infection) 042 Human immunodeficiency virus infection with specified conditions Includes: acquired immunodeficiency syndrome AIDS 042.0 With specified infections Includes only: candidiasis of lung (112.4) } coccidiosis (007.2) } cryptosporidiosis (007.2) } With isosporiasis (007.2) } HIV cryptococcosis (117.5) } infection pneumocystosis (136.3) } progressive multifocal leukoencephalopathy (046.3) } toxoplasmosis (130) } 042.1 Causing other specified infections Includes only: candidiasis } disseminated (112.5) } of: mouth (112.0) } skin and nails (112.3) } other and unspecified sites (112.8,112.9) } (excludes:112.1,112.2,112.4) } coccidioidomycosis (114) } cytomegalic inclusion disease (078.5) } herpes simplex (054) } herpes zoster (053) } histoplasmosis (115) } Due to mycobacteriosis, other and unspecified } HIV (031.8,031.9) (excludes: 031.0,031.1) } infection Nocardia infection (039) } opportunistic mycoses (118) } pneumonia: } NOS (486) } viral NOS (480.9) } Salmonella infections (003.1-003.9) } (excludes: gastroenteritis 003.0) } septicemia (038) } strongyloidiasis (127.2) } tuberculosis (010-018) } 042.2 With specified malignant neoplasms Includes only: Burkitt's tumor or lymphoma (200.2) } Kaposi's sarcoma (173) } Due to immunoblastic sarcoma (200.8) } HIV primary lymphoma of the brain (202.8) } infection reticulosarcoma (200.0) } 042.9 Acquired immunodeficiency syndrome, unspecified AIDS with other conditions classifiable elsewhere except as in 042.0-042.2 043 Human immunodeficiency virus infection causing other specified conditions Includes: AIDS-like syndrome AIDS-related complex ARC Excludes: HIV infection classifiable to 042 043.0 Causing lymphadenopathy Enlarged lymph nodes (785.6) } Due to HIV Swollen glands (785.6) } infection 043.1 Causing specified diseases of the central nervous system Includes only: central nervous system: } demyelinating disease NOS (341.9) } disorders NOS (348.9,349.9) } non-arthropod borne viral diseases, other } and unspecified (049.8,049.9) } slow virus infection, other and unspecified } (046.8,046.9) } dementia: } NOS (298.9) } Due to organic (294.9) } HIV presenile (290.1) } infection encephalitis (323.9) } encephalomyelitis (323.9) } encephalopathy (348.3) } myelitis (323.9) } myelopathy (336.9) } organic brain syndrome NOS } (nonpsychotic) (310.9) } psychotic (294.9) } 043.2 Causing other disorders involving the immune mechanism 043.3 Causing other specified conditions Includes only: abnormal weight loss (783.2) } abnormality,respiratory (786.0) } Due to agranulocytosis (288.0) } HIV anemia: } infection NOS (285.9) } aplastic, other and unspecified (284.8,284.9) } deficiency (280-281) } hemolytic, acquired (283) } arthritis: } pyogenic (711.0) } infective (711.9) } blindness or low vision (369) } blood and blood-forming organs, } unspecified disease (289.9) } cachexia (799.4) } dermatomycosis (111) } dermatophytosis (110) } diarrhea (noninfectious) (558), } infectious (009) } disease or disorder NOS: } Blood and blood-forming organs (289.9) } salivary gland (527.9) } skin and subcutaneous tissue (709.9) } dyspnea (786.0) } fatigue (780.7) } fever (780.6) } Due to gastroenteritis (noninfectious (558), } HIV infectious (009) } infection hepatomegaly (789.1) } hyperhidrosis (780.8) } hypersplenism (289.4) } infection: intestinal, ill-defined (009) } lack of expected physiological } development in infant (783.4) } leukoplakia of oral mucosa(tongue) (528.6) } malabsorption, intestinal (579.9) } malaise (780.7) } neuralgia NOS (729.2) } neuritis NOS (729.2) } nutritional deficiencies (260-269) } pneumonitis,lymphoid,interstitial (516.8) } polyneuropathy (357.0,357.8,357.9) } pyrexia (780.6) } radiculitis NOS (729.2) } rash NOS (782.1) } retinal vascular changes (362.1) } retinopathy, background (362.1) } splenomegaly (789.2) } thrombocytopenia, secondary and } unspecified (287.4,287.5) } volume depletion (276.5) } 043.9 Acquired immunodeficiency syndrome-related complex, unspecified AIDS-related complex (ARC) with other conditions classifiable elsewhere except as in 042.0-043.3 044 Other human immunodeficiency virus infection Excludes: HIV infection classifiable to 042 or 043 044.0 Causing specified acute infections Includes only: acute lymphadenitis (683) } Due aseptic meningitis (047.9) } to viral infection ("infectious mononucleosis-like } HIV syndrome") (079.9) } infection 044.9 Human immunodeficiency virus infection, unspecified HIV infection with other conditions classifiable elsewhere except as in 042.0-044.0 POLIOMYELITIS AND OTHER NON-ARTHROPOD-BORNE VIRAL DISEASES OF CENTRAL NERVOUS SYSTEM (045-049) 045 Acute poliomyelitis 045.0 Acute paralytic poliomyelitis specified as bulbar Infantile paralysis (acute) specified as bulbar Poliomyelitis (acute) (anterior) specified as bulbar Polioencephalitis (acute) (bulbar) Polioencephalomyelitis (acute) (anterior) (bulbar) 045.1 Acute poliomyelitis with other paralysis Paralysis: acute atrophic, spinal infantile, paralytic Poliomyelitis (acute) with paralysis except bulbar anterior with paralysis except bulbar epidemic with paralysis except bulbar 045.2 Acute nonparalytic poliomyelitis Poliomyelitis (acute) specified as nonparalytic anterior specified as nonparalytic epidemic specified as nonparalytic 045.9 Acute poliomyelitis, unspecified Infantile paralysis Poliomyelitis (acute) unspecified whether paralytic or nonparalytic anterior unspecified whether paralytic or nonparalytic epidemic unspecified whether paralytic or nonparalytic 046 Slow virus infection of central nervous system 046.0 Kuru 046.1 Jakob-Creutzfeldt disease Subacute spongioform encephalopathy 046.2 Subacute sclerosing panencephalitis Dawson's inclusion body encephalitis Van Bogaert's sclerosing leucoencephalitis 046.3 Progressive multifocal leucoencephalopathy Multifocal leucoencephalopathy NOS 046.8 Other 046.9 Unspecified 047 Meningitis due to enterovirus Includes: meningitis: abacterial aseptic viral Excludes: meningitis due to: adenovirus (049.1) arthropod-borne virus (060-066) leptospira (100.8) virus of: herpes simplex (054.7) herpes zoster (053.0) lymphocytic choriomeningitis (049.0) mumps (072.1) poliomyelitis (045.-) any other infection specifically classified elsewhere 047.0 Coxsackie virus 047.1 ECHO virus 047.8 Other 047.9 Unspecified Viral meningitis NOS 048 Other enterovirus diseases of central nervous system Boston exanthem 049 Other non-arthropod-borne viral diseases of central nervous system 049.0 Lymphocytic choriomeningitis Lymphocytic: meningitis (serous) meningoencephalitis (serous) 049.1 Meningitis due to adenovirus 049.8 Other Encephalitis: acute: inclusion body necrotizing epidemic lethargica Rio Bravo von Economo's disease 049.9 Unspecified Viral encephalitis NOS VIRAL DISEASES ACCOMPANIED BY EXANTHEM (050-057) Excludes: arthropod-borne viral diseases (060-066) 050 Smallpox 050.0 Variola major Hemorrhagic (pustular) smallpox Malignant smallpox Purpura variolosa 050.1 Alastrim Variola minor 050.2 Modified smallpox 050.9 Smallpox, unspecified 051 Cowpox and paravaccinia 051.0 Cowpox Vaccinia not from vaccination Excludes: vaccinia (generalized) (from vaccination) (999.0) 051.1 Pseudocowpox Milkers' node 051.2 Contagious pustular dermatitis Ecthyma contagiosum Orf 051.9 Paravaccinia, unspecified 052 Chickenpox Varicella 053 Herpes zoster Includes: shingles zona 053.0 With meningitis 053.1 With other nervous system complications Geniculate herpes zoster Post-herpetic: Herpetic geniculate ganglionitis polyneuropathy trigeminal neuralgia 053.2 With ophthalmic complications Herpes zoster: dermatitis of eyelids iridocyclitis keratoconjunctivitis 053.7 With other complications 053.8 With unspecified complication 053.9 Herpes zoster without mention of complication 054 Herpes simplex Excludes: congenital herpes simplex (771.2) 054.0 Eczema herpeticum Kaposi's varicelliform eruption 054.1 Genital herpes Herpetic vulvovaginitis Herpetic ulceration of vulva 054.2 Herpetic gingivostomatitis 054.3 Herpetic meningoencephalitis Herpes encephalitis Simian B disease 054.4 With ophthalmic complications Herpes simplex: Keratitis: dermatitis of eyelids dendritic keratitis disciform keratoconjunctivitis Iritis due to herpes simplex 054.5 Herpetic septicaemia 054.6 Herpetic whitlow 054.7 With other complications Meningitis due to herpes simplex Visceral herpes simplex 054.8 With unspecified complication 054.9 Herpes simplex without mention of complication 055 Measles Includes: morbilli rubeola 055.0 Postmeasles encephalitis 055.1 Postmeasles pneumonia 055.2 Postmeasles otitis 055.7 With other complications 055.8 With unspecified complication 055.9 Measles without mention of complication 056 Rubella Includes: German measles Excludes: congenital rubella (771.0) 056.0 With neurological complications Encephalomyelitis 056.7 With other complications Rubella arthritis 056.8 With unspecified complications 056.9 Rubella without mention of complication 057 Other viral exanthemata 057.0 Erythema infectiosum [fifth disease] 057.8 Other Dukes(-Filatow) disease Exanthema subitum Fourth disease Parascarlatina Pseudoscarlatina Roseola infantum Sixth disease 057.9 Unspecified ARTHROPOD-BORNE VIRAL DISEASES (060-066) 060 Yellow fever 060.0 Sylvatic Jungle yellow fever 060.1 Urban 060.9 Unspecified 061 Dengue Breakbone fever Excludes: hemorrhagic fever caused by dengue virus (065.4) 062 Mosquito-borne viral encephalitis 062.0 Japanese encephalitis 062.1 Western equine encephalitis 062.2 Eastern equine encephalitis Excludes: Venezuelan equine encephalitis (066.2) 062.3 St. Louis encephalitis 062.4 Australian encephalitis Australian arboencephalitis Australian X disease 062.5 California virus encephalitis Encephalitis: California La Crosse Tahyna fever 062.8 Other Encephalitis by Ilheus virus 062.9 Unspecified 063 Tick-borne viral encephalitis Includes: diphasic meningoencephalitis 063.0 Russian spring-summer [taiga] encephalitis 063.1 Louping ill 063.2 Central European encephalitis 063.8 Other Langat encephalitis Powassan encephalitis 063.9 Unspecified 064 Viral encephalitis transmitted by other and unspecified arthropods Arthropod-borne viral encephalitis, vector unknown Negishi virus encephalitis Excludes: viral encephalitis NOS (049.9) 065 Arthropod-borne hemorrhagic fever 065.0 Crimean hemorrhagic fever [CHF Congo virus] Central Asian hemorrhagic fever 065.1 Omsk hemorrhagic fever 065.2 Kyasanur Forest disease 065.3 Other tick-borne hemorrhagic fever 065.4 Mosquito-borne hemorrhagic fever Chikungunya hemorrhagic fever Dengue hemorrhagic fever Excludes: Chikungunya fever (066.3) dengue (061) yellow fever (060.-) 065.8 Other 065.9 Unspecified Arbovirus hemorrhagic fever NOS 066 Other arthropod-borne viral diseases 066.0 Phlebotomus fever Changuinola fever Sandfly fever 066.1 Tick-borne fever Nairobi sheep disease Tick fever: Tick fever: American mountain Kemerovo Colorado Quaranfil 066.2 Venezuelan equine fever 066.3 Other mosquito-borne fever Fever (viral): Fever (viral): Bunyamwera Oropouche Bwamba Pixuna Chikungunya Rift valley Guama Wesselsbron Mayaro West Nile Mucambo Zika O'nyong-Nyong Excludes: dengue (061) yellow fever (060.-) 066.8 Other Chandipura fever Piry fever 066.9 Unspecified Arbovirus infection NOS OTHER DISEASES DUE TO VIRUSES AND CHLAMYDIAE (070-079) 070 Viral hepatitis Excludes: cytomegalic inclusion virus hepatitis (078.5) 070.0 Viral hepatitis A with hepatic coma 070.1 Viral hepatitis A without mention of hepatic coma Infectious hepatitis 070.2 Viral hepatitis B with hepatic coma 070.3 Viral hepatitis B without mention of hepatic coma Serum hepatitis 070.4 Other specified viral hepatitis with hepatic coma 070.5 Other specified viral hepatitis without mention of hepatic coma 070.6 Unspecified viral hepatitis with hepatic coma 070.9 Unspecified viral hepatitis without mention of hepatic coma Viral hepatitis NOS 071 Rabies Hydrophobia Lyssa 072 Mumps 072.0 Mumps orchitis 072.1 Mumps meningitis 072.2 Mumps encephalitis Mumps meningoencephalitis 072.3 Mumps pancreatitis 072.7 Mumps with other complications 072.8 Mumps with unspecified complication 072.9 Mumps without mention of complication Epidemic parotitis Infectious parotitis 073 Ornithosis Parrot fever Psittacosis 074 Specific diseases due to Coxsackie virus Excludes: Coxsackie virus: infection NOS (079.2) meningitis (047.0) 074.0 Herpangina Vesicular pharyngitis 074.1 Epidemic pleurodynia Bornholm disease Devil's grip Epidemic: myalgia myositis 074.2 Coxsackie carditis Aseptic myocarditis of newborn Coxsackie: endocarditis myocarditis pericarditis 074.3 Hand, foot and mouth disease Vesicular stomatitis and exanthem 074.8 Other Acute lymphonodular pharyngitis 075 Infectious mononucleosis Glandular fever Monocytic angina Pfeiffer's disease 076 Trachoma Excludes: late effect of trachoma; see category 139.1 076.0 Initial stage Trachoma dubium 076.1 Active stage Granular conjunctivitis Trachomatous: (trachomatous) follicular conjunctivitis pannus 076.9 Unspecified Trachoma NOS 077 Other diseases of conjunctiva due to viruses and Chlamydiae Excludes: ophthalmic complications of viral diseases classified elsewhere 077.0 Inclusion conjunctivitis Paratrachoma Swimming pool conjunctivitis Excludes: inclusion blennorrhoea (neonatal) (771.6) 077.1 Epidemic keratoconjunctivitis Shipyard eye 077.2 Pharyngoconjunctival fever Viral pharyngoconjunctivitis 077.3 Other adenoviral conjunctivitis Acute adenoviral follicular conjunctivitis 077.4 Epidemic hemorrhagic conjunctivitis Apollo: conjunctivitis disease Conjunctivitis due to enterovirus type 70 Hemorrhagic conjunctivitis (acute) (epidemic) 077.8 Other viral conjunctivitis Newcastle conjunctivitis 077.9 Unspecified Viral conjunctivitis NOS 078 Other diseases due to viruses and Chlamydiae Excludes: Viral infection NOS (079.-) Viraemia NOS (790.8) 078.0 Molluscum contagiosum 078.1 Viral warts Condyloma acuminatum Verruca (vulgaris) (plana) (plantaris) Warts (infectious) 078.2 Sweating fever Miliary fever Sweating disease 078.3 Cat-scratch disease Benign lymphoreticulosis (of inoculation) Cat-scratch fever 078.4 Foot and mouth disease Epizootic: aphthae stomatitis 078.5 Cytomegalic inclusion disease Cytomegalic inclusion virus hepatitis Salivary gland virus disease Excludes: congenital cytomegalovirus infection (771.1) 078.6 Hemorrhagic nephrosonephritis Hemorrhagic fever: epidemic Korean Russian with renal syndrome 078.7 Arenaviral hemorrhagic fever Hemorrhagic fever: Argentine Bolivian Junin virus Machupo virus 078.8 Other Epidemic: Marburg disease cervical myalgia Tanapox vertigo Winter vomiting disease vomiting syndrome 079 Viral infection in conditions classified elsewhere and of unspecified site Note: This category will rarely be used for primary coding. It is provided as an additional code where it is desired to identify the viral agent in diseases classified elsewhere. This category will also be used in primary coding to classify virus infection of unspecified nature or site. 079.0 Adenovirus 079.1 ECHO virus 079.2 Coxsackie virus 079.3 Rhinovirus 079.8 Other 079.9 Unspecified Viral infection NOS Excludes: viraemia NOS (790.8) RICKETTSIOSES AND OTHER ARTHROPOD-BORNE DISEASES (080-088) Excludes: arthropod-borne viral diseases (060-066) 080 Louse-borne [epidemic] typhus Typhus (fever): classical epidemic exanthematic NOS louse-borne 081 Other typhus 081.0 Murine [endemic] typhus Typhus (fever): endemic flea-borne 081.1 Brill's disease Brill-Zinsser disease Recrudescent typhus (fever) 081.2 Scrub typhus Japanese river fever Mite-borne typhus Kedani fever Tsutsugamushi 081.9 Unspecified Typhus (fever) NOS 082 Tick-borne rickettsioses 082.0 Spotted fevers Rocky mountain spotted fever Sao Paulo fever 082.1 Boutonneuse fever African tick typhus Marseilles fever India tick typhus Mediterranean tick fever Kenya tick typhus 082.2 North Asian tick fever Siberian tick typhus 082.3 Queensland tick typhus 082.8 Other Lone star fever 082.9 Unspecified Tick-borne typhus NOS 083 Other rickettsioses 083.0 Q-fever 083.1 Trench fever Quintan fever Wolhynian fever 083.2 Rickettsialpox Vesicular rickettsiosis 083.8 Other 083.9 Unspecified 084 Malaria Excludes: congenital malaria (771.2) Note: Subcategories 084.0-084.6 exclude the listed conditions with mention of pernicious complications (084.8, 084.9). 084.0 Falciparum malaria [malignant tertian] Malaria (fever): by Plasmodium falciparum subtertian 084.1 Vivax malaria [benign tertian] Malaria (fever) by Plasmodium vivax 084.2 Quartan malaria Malaria (fever) by Plasmodium malariae Malariae malaria 084.3 Ovale malaria Malaria (fever) by Plasmodium ovale 084.4 Other malaria Monkey malaria 084.5 Mixed Malaria (fever) by more than one parasite 084.6 Unspecified Malaria (fever) NOS 084.7 Induced malaria Therapeutically induced malaria Excludes: accidental infection from syringe, blood transfusion, etc. (084.0-084.6, above, according to parasite species) transmission from mother to child during delivery (771.2) 084.8 Blackwater fever Hemoglobinuric: Malarial hemoglobinuria fever (bilious) malaria 084.9 Other pernicious complications of malaria Algid malaria Malarial: Cerebral malaria hepatitis nephrosis 085 Leishmaniasis 085.0 Visceral [kala-azar] Dumdum fever Leishmaniasis: Infection by Leishmania: dermal, post-kala-azar donovani Mediterranean infantum visceral (Indian) 085.1 Cutaneous, urban Aleppo boil Leishmaniasis, cutaneous: Baghdad boil dry form Delhi boil late Infection by Leishmania tropica recurrent Oriental sore ulcerating 085.2 Cutaneous, Asian desert Infection by Leishmania tropica major Leishmaniasis, cutaneous: Leishmaniasis, cutaneous: acute necrotizing wet form rural zoonotic form 085.3 Cutaneous, Ethiopian Infection by Leishmania ethiopica Leishmaniasis, cutaneous: diffuse lepromatous 085.4 Cutaneous, American Chiclero ulcer Infection by Leishmania mexicana Leishmaniasis tegumentaria diffusa 085.5 Mucocutaneous (American) Espundia Uta Infection by Leishmania brasiliensis 085.9 Unspecified 086 Trypanosomiasis Includes: with meningoencephalitis 086.0 Chagas's disease with heart involvement Any condition in 086.2 with heart involvement 086.1 Chagas's disease with other organ involvement Any condition in 086.2 with involvement of organ other than heart 086.2 Chagas's disease without mention of organ involvement American trypanosomiasis Infection by Trypanosoma cruzi 086.3 Gambian trypanosomiasis Gambian sleeping sickness Infection by Trypanosoma gambiense 086.4 Rhodesian trypanosomiasis Infection by Trypanosoma rhodesiense Rhodesian sleeping sickness 086.5 African trypanosomiasis, unspecified Sleeping sickness NOS 086.9 Unspecified 087 Relapsing fever Recurrent fever 087.0 Louse-borne 087.1 Tick-borne 087.9 Unspecified 088 Other arthropod-borne diseases 088.0 Bartonellosis Carrion's disease Oroya fever Verruga peruana 088.8 Other 088.9 Unspecified Arthropod-borne disease, not elsewhere classified SYPHILIS AND OTHER VENEREAL DISEASES (090-099) Excludes: nonvenereal endemic syphilis (104.0) urogenital trichomoniasis (131.0) 090 Congenital syphilis 090.0 Early congenital syphilis, symptomatic Congenital syphilitic: Syphilitic (congenital): choroiditis epiphysitis coryza (chronic) osteochondritis hepatomegaly pemphigus mucous patches Any congenital syphilitic condition periostitis specified as early or manifest less splenomegaly than two years after birth 090.1 Early congenital syphilis, latent [Not to be used for underlying cause of death] Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after birth 090.2 Early congenital syphilis, unspecified Congenital syphilis NOS, less than two years after birth 090.3 Syphilitic interstitial keratitis Syphilitic keratitis: parenchymatous punctata profunda Excludes: interstitial keratitis NOS (370.5) 090.4 Juvenile neurosyphilis Congenital: Dementia paralytica juvenilis neurosyphilis Juvenile: syphilitic: general paresis encephalitis tabes meningitis taboparesis Use additional code, if desired, to identify any associated mental disorder. 090.5 Other late congenital syphilis, symptomatic Gumma due to congenital syphilis Hutchinson's teeth Syphilitic saddle nose Any congenital syphilitic condition specified as late or manifest two years or more after birth 090.6 Late congenital syphilis, latent [Not to be used for underlying cause of death] Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after birth 090.7 Late congenital syphilis, unspecified Congenital syphilis NOS, two years or more after birth 090.9 Congenital syphilis, unspecified 091 Early syphilis, symptomatic Excludes: early cardiovascular syphilis (093.-) early neurosyphilis (094.-) 091.0 Genital syphilis (primary) Genital chancre 091.1 Primary anal syphilis 091.2 Other primary syphilis Primary syphilis of: fingers lip tonsils 091.3 Secondary syphilis of skin or mucous membranes Condyloma latum Secondary syphilis of: Secondary syphilis of: anus skin mouth tonsils pharynx vulva 091.4 Adenopathy due to secondary syphilis Syphilitic adenopathy (secondary) Syphilitic lymphadenitis (secondary) 091.5 Uveitis due to secondary syphilis Syphilitic chorioretinitis (secondary) Syphilitic iridocyclitis (secondary) 091.6 Secondary syphilis of viscera and bone Secondary syphilis of liver Secondary syphilitic: Secondary syphilitic: hepatitis periostitis 091.7 Secondary syphilis, relapse Secondary syphilis, relapse (treated) (untreated) 091.8 Other forms of secondary syphilis Acute syphilitic meningitis Syphilitic alopecia 091.9 Unspecified secondary syphilis 092 Early syphilis, latent [Not to be used for underlying cause of death] Includes: syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after infection 092.0 Early syphilis, latent, serological relapse after treatment 092.9 Early syphilis, latent, unspecified 093 Cardiovascular syphilis 093.0 Aneurysm of aorta, specified as syphilitic Dilatation of aorta, specified as syphilitic 093.1 Syphilitic aortitis 093.2 Syphilitic endocarditis Syphilitic: aortic incompetence or stenosis ostial coronary disease 093.8 Other Syphilitic: myocarditis pericarditis 093.9 Unspecified 094 Neurosyphilis 094.0 Tabes dorsalis Arthropathy: neurogenic (Charcot) tabetic Charcot's joint disease Locomotor ataxia (progressive) Posterior spinal sclerosis (syphilitic) Tabetic neurosyphilis 094.1 General paresis Dementia paralytica General paralysis (of insane) (progressive) Paretic neurosyphilis Taboparesis 094.2 Syphilitic meningitis Meningovascular syphilis 094.3 Asymptomatic neurosyphilis [Not to be used for underlying cause of death] 094.8 Other Syphilitic: acoustic neuritis disseminated retinochoroiditis encephalitis optic atrophy Parkinsonism retrobulbar neuritis ruptured cerebral aneurysm 094.9 Unspecified Gumma (syphilitic) of central nervous system NOS Syphilis (early) (late) of central nervous system NOS Syphiloma of central nervous system NOS 095 Other forms of late syphilis, with symptoms Gumma (syphilitic) } any site except those classifiable in Syphilis, late or tertiary } 093.- and 094.- Gumma (syphilitic) NOS Syphilis [stage unspecified]: Syphilitic: bone episcleritis kidney peritonitis liver lung muscle 096 Late syphilis, latent [Not to be used for underlying cause of death] Syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after infection 097 Other and unspecified syphilis 097.0 Late syphilis, unspecified 097.1 Latent syphilis, unspecified [Not to be used for underlying cause of death] Positive serological reaction for syphilis 097.9 Syphilis, unspecified Syphilis (acquired) NOS Excludes: syphilis NOS causing death under two years of age (090.9) 098 Gonococcal infections 098.0 Acute, of lower genitourinary tract Gonococcal: Gonorrhea (acute): Bartholinitis (acute) NOS urethritis (acute) genitourinary (tract) NOS vulvovaginitis (acute) 098.1 Acute, of upper genitourinary tract Gonococcal: Gonorrhea (acute): endometritis (acute) bladder orchitis (acute) cervix prostatitis (acute) seminal vesicle salpingitis, acute 098.2 Chronic, of lower genitourinary tract Any condition in 098.0 specified as chronic or with duration of two months or over 098.3 Chronic, of upper genitourinary tract Any condition in 098.1 specified as chronic or with duration of two months or over Gonococcal salpingitis (chronic) 098.4 Of eye Gonococcal: conjunctivitis (neonatorum) iridocyclitis (364.0*) ophthalmia (neonatorum) 098.5 Of joint Gonococcal: Gonococcal: arthritis synovitis bursitis tenosynovitis 098.6 Of pharynx 098.7 Of anus and rectum 098.8 Of other sites Gonococcaemia Gonococcal: Gonococcal: meningitis endocarditis peritonitis keratosis (blenorrhagica) 099 Other venereal diseases 099.0 Chancroid Bubo (inguinal): Chancre: chancroidal Ducrey's due to Hemophilus ducreyi simple Ulcus molle (cutis) (skin) soft 099.1 Lymphogranuloma venereum Climatic or tropical bubo (Durand-) Nicolas-Favre disease Esthiomene Lymphogranuloma inguinale 099.2 Granuloma inguinale Donovanosis Granuloma pudendi (ulcerating) Granuloma venereum 099.3 Reiter's disease Reiter's syndrome 099.4 Other nongonococcal urethritis Nonspecific and nongonococcal urethritis so stated 099.8 Other 099.9 Unspecified OTHER SPIROCHETAL DISEASES (100-104) 100 Leptospirosis 100.0 Leptospirosis icterohemorrhagica Leptospiral or spirochetal jaundice (hemorrhagic) Weil's disease 100.8 Other Fever: Fort Bragg pretibial swamp Infection by Leptospira: australis bataviae pyrogenes Leptospiral meningitis (aseptic) 100.9 Unspecified 101 Vincent's angina Acute necrotizing ulcerative: gingivitis stomatitis Fusospirochaetal pharyngitis Spirochetal stomatitis Trench mouth Vincent's: gingivitis infection [any site] 102 Yaws Includes: frambesia pian 102.0 Initial lesions Chancre of yaws Initial framboesial ulcer Framboesia, initial or primary Mother yaw 102.1 Multiple papillomata and wet crab yaws Butter yaws Framboesioma Pianoma Plantar or palmar papilloma of yaws 102.2 Other early skin lesions Early yaws (cutaneous) (macular) (papular) (maculopapular) (micropapular) Framboeside of early yaws Cutaneous yaws, less than five years after infection 102.3 Hyperkeratosis Ghoul hand Hyperkeratosis, palmar or plantar (early) (late) due to yaws Worm-eaten soles 102.4 Gummata and ulcers Nodular late yaws (ulcerated) Gummatous framboeside 102.5 Gangosa Rhinopharyngitis mutilans 102.6 Bone and joint lesions Goundou of yaws (late) Gumma, bone of yaws (late) Gummatous osteitis or periostitis of yaws (late) Ganglion Hydrarthrosis of yaws (early) (late) Osteitis of yaws (early) (late) Periostitis (hypertrophic) of yaws (early) (late) 102.7 Other manifestations Juxta-articular nodules of yaws Mucosal yaws 102.8 Latent yaws [Not to be used for underlying cause of death] Yaws without clinical manifestations, with positive serology 102.9 Yaws, unspecified 103 Pinta 103.0 Primary lesions Chancre (primary) of pinta [carate] Papule (primary) of pinta [carate] Pintid of pinta [carate] 103.1 Intermediate lesions Erythematous plaques of pinta [carate] Hyperchromic lesions of pinta [carate] Hyperkeratosis of pinta [carate] 103.2 Late lesions Cardiovascular lesions of pinta [carate] Skin lesions of pinta [carate]: achromic of pinta [carate] cicatricial of pinta [carate] dyschromic of pinta [carate] Vitiligo of pinta [carate] 103.3 Mixed lesions Achromic and hyperchromic skin lesions of pinta [carate] 103.9 Unspecified 104 Other spirochaetal infection 104.0 Nonvenereal endemic syphilis Bejel Njovera 104.8 Other Excludes: relapsing fever (087.-) syphilis (090-097) 104.9 Unspecified MYCOSES (110-118) Excludes: infection by Actinomycetales such as species of Actinomyces, Actinomadura, Nocardia, Streptomyces (039.-) 110 Dermatophytosis Includes: infection by species of Epidermophyton, Microsporum, and Trichophyton tinea, any type except those in 111 110.0 Of scalp and beard Kerion Sycosis, mycotic Trichophytic tinea scalp [black dot tinea] 110.1 Of nail Dermatophytic onychia Onychomycosis Tinea unguium 110.2 Of hand Tinea manuum 110.3 Of groin and perianal area Dhobie itch Eczema marginatum 110.4 Of foot Athlete's foot Tinea pedis 110.5 Of the body Herpes circinatus Tinea imbricata [Tokelau] 110.6 Deep seated dermatophytosis Granuloma trichophyticum Majocchi's granuloma 110.8 Of other sites 110.9 Of unspecified site Favus NOS Microsporic tinea NOS Ringworm NOS 111 Dermatomycosis, other and unspecified 111.0 Pityriasis versicolor Infection by Malassezia [Pityrosporum] furfur Tinea flava Tinea versicolor 111.1 Tinea nigra Infection by Cladosporium species Keratomycosis nigricans Microsporosis nigra Pityriasis nigra Tinea palmaris nigra 111.2 Tinea blanca Infection by Trichosporon (beigelii) cutaneum White piedra 111.3 Black piedra Infection by Piedraia hortai 111.8 Other 111.9 Unspecified 112 Candidiasis Includes: infection by Candida species candidiasis moniliasis Excludes: neonatal monilial infection (771.7) 112.0 Of mouth Thrush 112.1 Of vulva and vagina Candidal vulvovaginitis Monilial vulvovaginitis 112.2 Of other urogenital sites 112.3 Of skin and nails Candidal intertrigo Candidal perionyxis [paronychia] Candidal onychia 112.4 Of lung 112.5 Disseminated Systemic candidiasis 112.8 Of other sites Candidal endocarditis 112.9 Of unspecified site 114 Coccidioidomycosis Coccidioidal granuloma Posada-Wernicke disease Desert rheumatism San Joaquin Valley fever Infection by Coccidioides (immitis) 115 Histoplasmosis 115.0 Infection by Histoplasma capsulatum American histoplasmosis Reticuloendothelial cytomycosis Darling's disease Small form histoplasmosis 115.1 Infection by Histoplasma duboisii African histoplasmosis Large form histoplasmosis 115.9 Unspecified Histoplasmosis NOS 116 Blastomycotic infection 116.0 Blastomycosis Blastomycetic dermatitis Chicago disease Cutaneous blastomycosis Disseminated blastomycosis Gilchrist's disease Infection by Blastomyces [Ajellomyces] dermatitidis North American blastomycosis Primary pulmonary blastomycosis 116.1 Paracoccidioidomycosis Brazilian blastomycosis Infection by Paracoccidioides [Blastomyces] brasiliensis Lutz-Splendore-Almeida disease Mucocutaneous-lymphangitic paracoccidioidomycosis Pulmonary paracoccidioidomycosis South American blastomycosis Visceral paracoccidioidomycosis 116.2 Lobomycosis Infections by Loboa [Blastomyces] loboi Keloidal blastomycosis Lobo's disease 117 Other mycoses 117.0 Rhinosporidiosis Infection by Rhinosporidium seeberi 117.1 Sporotrichosis Cutaneous sporotrichosis Disseminated sporotrichosis Infection by Sporothrix [Sporotrichum] schenckii Lymphocutaneous sporotrichosis Pulmonary sporotrichosis Sporotrichosis of the bones 117.2 Chromoblastomycosis Chromomycosis Infection by Cladosporidium carrionii, Fonsecaea compactum, Fonsecaea pedrosoi, Phialophora verrucosa 117.3 Aspergillosis Infection by Aspergillus species, mainly A. fumigatus, A. flavus group, A. terreus group 117.4 Mycotic mycetomas Infection by various genera and species of Ascomycetes and Deuteromycetes, such as Acremonium [Cephalosporium] falciforme, Neotestudina rosatii, Madurella grisea, Madurella mycetomii, Pyrenochaeta romeroi, Zopfia [Leptosphaeria] senegalensis Madura foot, mycotic Maduromycosis, mycotic Excludes: actinomycotic mycetomas (039.-) 117.5 Cryptococcosis Busse-Buschke's disease Pulmonary cryptococcosis Cryptococcal meningitis Systemic cryptococcosis European cryptococcosis Torula Infection by Cryptococcus neoformans 117.6 Allescheriosis [Petriellidosis] Infections by Allescheria [Petriellidium] boydii [Monosporium apiospermum] Excludes: mycotic mycetoma (117.4) 117.7 Zygomycosis [Phycomycosis or Mucormycosis] Infection by species of Absidia, Basidiobolus, Conidiobolus, Cunninghamella, Entomophthora, Mucor, Rhizopus, Saksenaea 117.8 Infection by dematiacious fungi [Phaehyphomycosis] Infection by dematiacious fungi such as Cladosporium trichoides [bantianum], Dreschlera hawaiiensis, Phialophora gougerotii, Phialophora jeanselmei 117.9 Other and unspecified 118 Opportunistic mycoses Infection of skin, subcutaneous tissues and/or organs by a wide variety of fungi generally considered to be pathogenic to compromised hosts only, e.g., infection by species of Alternaria, Dreschlera, Fusarium HELMINTHIASES (120-129) 120 Schistosomiasis[bilharziasis] 120.0 Schistosoma haematobium Vesical schistosomiasis NOS 120.1 Schistosoma mansoni Intestinal schistosomiasis NOS 120.2 Schistosoma japonicum Asiatic schistosomiasis NOS Katayama disease or fever 120.3 Cutaneous Cercarial dermatitis Infection by cercariae of Schistosoma Schistosome dermatitis 120.8 Other Infection by Schistosoma: bovis intercalatum mattheii Spindale Schistosomiasis chestermani 120.9 Unspecified Blood flukes NOS Haemic distomiasis 121 Other trematode infections 121.0 Opisthorchiasis Infection by: cat liver fluke Opisthorchis (felineus) (tenuicollis) (viverrini) 121.1 Clonorchiasis Biliary cirrhosis due to clonorchiasis Chinese liver fluke disease Hepatic distomiasis due to Clonorchis sinensis Oriental liver fluke disease 121.2 Paragonimiasis Infection by Paragonimus Lung fluke disease (oriental) Pulmonary distomiasis 121.3 Fascioliasis Infection by Fasciola: gigantica hepatica Liver flukes NOS Sheep liver fluke infection 121.4 Fasciolopsiasis Infection by Fasciolopsis (buski) Intestinal distomiasis 121.5 Metagonimiasis Infection by Metagonimus yokogawai 121.6 Heterophyiasis Infection by: Heterophyes heterophyes Stellantchasmus falcatus 121.8 Other Infection by: Dicrocoelium dendriticum Echinostomum ilocanum Gastrodiscoides hominis 121.9 Unspecified Distomiasis NOS Fluke disease NOS 122 Echinococcosis Includes: echinococciasis hydatid disease hydatidosis 122.0 Echinococcus granulosus infection of liver 122.1 Echinococcus granulosus infection of lung 122.2 Echinococcus granulosus infection of thyroid 122.3 Echinococcus granulosus infection, other 122.4 Echinococcus granulosus infection, unspecified 122.5 Echinococcus multilocularis infection of liver 122.6 Echinococcus multilocularis infection, other 122.7 Echinococcus multilocularis infection, unspecified 122.8 Echinococcosis, unspecified, of liver 122.9 Echinococcosis, other and unspecified 123 Other cestode infection 123.0 Taenia solium infection, intestinal form Pork tapeworm (adult) (infection) 123.1 Cysticercosis Cysticerciasis Infection by: Cysticercus cellulosae [larval form of Taenia solium] 123.2 Taenia saginata infection Beef tapeworm (infection) Infection by Taeniarhyuchus saginatus 123.3 Taeniasis, unspecified 123.4 Diphyllobothriasis, intestinal Diphyllobothrium (adult) (latum) (pacificum) infection Fish tapeworm (infection) 123.5 Sparganosis [larval diphyllobothriasis] Infection by: Diphyllobothrium larvae Sparganum (mansoni) (proliferum) Spirometra larvae 123.6 Hymenolepiasis Dwarf tapeworm (infection) Hymenolepis (diminuta) (nana) infection Rat tapeworm (infection) 123.8 Other Diplogonoporus (grandis) infection Dipylidium (caninum) infection Dog tapeworm (infection) 123.9 Unspecified Tapeworm (infection) NOS 124 Trichinosis Trichinella spiralis infection Trichinellosis Trichiniasis 125 Filarial infection and dracontiasis 125.0 Bancroftian filariasis Chyluria due to Wuchereria bancrofti Elephantiasis due to Wuchereria bancrofti Infection due to Wuchereria bancrofti Lymphadenitis due to Wuchereria bancrofti Lymphangitis due to Wuchereria bancrofti Wuchereriasis due to Wuchereria bancrofti 125.1 Malayan filariasis Brugia filariasis due to Brugia [Wuchereria] malayi Chyluria due to Brugia [Wuchereria] malayi Elephantiasis due to Brugia [Wuchereria] malayi Infection due to Brugia [Wuchereria] malayi Lymphadenitis due to Brugia [Wuchereria] malayi Lymphangitis due to Brugia [Wuchereria] malayi 125.2 Loiasis Eyeworm disease of Africa Loa loa infection 125.3 Onchocerciasis Onchocerca volvulus infection Onchocercosis 125.4 Dipetalonemiasis Infection by: Acanthocheilonema perstans Dipetalonema perstans 125.5 Mansonella ozzardi infection Filariasis ozzardi 125.6 Other specified filariasis Dirofilaria infection Infection by: Acanthocheilonema streptocerca Dipetalonema streptocerca 125.7 Dracontiasis Guinea-worm infection Infection by Dracunculus medinensis 125.9 Unspecified filariasis 126 Ancylostomiasis and necatoriasis Includes: cutaneous larva migrans due to Ancylostoma hookworm (disease) (infection) uncinariasis 126.0 Ancylostoma duodenale 126.1 Necator americanus 126.2 Ancylostoma braziliense 126.3 Ancylostoma ceylanicum 126.8 Other specified Ancylostoma 126.9 Unspecified Creeping eruption NOS Cutaneous larva migrans NOS 127 Other intestinal helminthiases 127.0 Ascariasis Ascaridiasis Infection by Ascaris lumbricoides Roundworm infection 127.1 Anisakiasis Infection by Anisakis larva 127.2 Strongyloidiasis Infection by Strongyloides stercoralis Excludes: trichostrongyliasis (127.6) 127.3 Trichuriasis Infection by Trichuris trichiura Trichocephaliasis Whipworm (disease) (infection) 127.4 Enterobiasis Infection by Enterobius vermicularis Oxyuriasis Oxyuris vermicularis infection Pinworm (disease) (infection) Threadworm infection 127.5 Capillariasis Infection by Capillaria philippinensis Excludes: infection by Capillaria hepatica (128.8) 127.6 Trichostrongyliasis Infection by Trichostrongylus species 127.7 Other intestinal helminthiasis Infection by: Oesophagostomum apiostomum and related species Ternidens diminutus other specified intestinal helminth Physalopteriasis 127.8 Mixed intestinal helminthiasis Infection by intestinal helminths classified to more than one of the categories 120.0-127.7 Mixed helminthiasis NOS 127.9 Intestinal helminthiasis, unspecified 128 Other and unspecified helminthiases 128.0 Toxocariasis Larva migrans visceralis Toxocara (canis) (cati) infection Visceral larva migrans syndrome 128.1 Gnathostomiasis Infection by Gnathostoma spinigerum and related species 128.8 Other Infection by: Angiostrongylus cantonensis Capillaria hepatica other specified helminth 128.9 Unspecified Helminthiasis NOS Worms NOS 129 Intestinal parasitism, unspecified OTHER INFECTIOUS AND PARASITIC DISEASES (130-136) 130 Toxoplasmosis Infection by Toxoplasma gondii Chorioretinitis } Hepatitis } Meningoencephalitis } Due to acquired toxoplasmosis Myocarditis } Pneumonitis } Excludes: congenital toxoplasmosis (771.2) 131 Trichomoniasis 131.0 Urogenital trichomoniasis Fluor (vaginalis) } Leukorrhoea (vaginalis) } Prostatitis } trichomonal or due to Trichomonas (vaginalis) Urethritis } Vaginitis } Vulvovaginitis } 131.8 Other sites Excludes: intestinal (007.3) 131.9 Unspecified 132 Pediculosis and phthirus infestation 132.0 Pediculus capitis [head louse] 132.1 Pediculus corporis [body louse] 132.2 Phthirus pubis [pubic louse] 132.3 Mixed Infestation classifiable to more than one of the categories 132.0-132.2 132.9 Pediculosis, unspecified 133 Acariasis 133.0 Scabies Infestation by Sarcoptes scabiei Sarcoptic itch 133.8 Other Chiggers Infestation by: Demodex folliculorum Trombiculae 133.9 Unspecified Infestation by mites NOS 134 Other infestation 134.0 Myiasis Infestation by: Infestation by: Dermatobia (hominis) maggots fly larvae Oestrus ovis Gasterophilus (intestinalis) 134.1 Other arthropod infestation Infestation by: chigoe sand flea Tunga penetrans Jigger disease Scarabiasis 134.2 Hirudiniasis Hirudiniasis (external) (internal) Leeches (aquatic) (land) 134.8 Other 134.9 Unspecified Infestation (skin) NOS Skin parasites NOS 135 Sarcoidosis Besnier-Boeck-Schaumann disease Lupoid (miliary) of Boeck Lupus pernio (Besnier) Lymphogranulomatosis, benign (Schaumann) Sarcoid (any site): NOS Boeck Darier-Roussy Uveoparotid fever 136 Other and unspecified infectious and parasitic diseases 136.0 Ainhum Dactylolysis spontanea 136.1 Behcet's syndrome 136.2 Specific infections by free-living amoebae Meningoencephalitis due to Naegleria 136.3 Pneumocystosis Pneumonia due to Pneumocystis carinii 136.4 Psorospermiasis 136.5 Sarcosporidiosis 136.8 Other Candiru infestation 136.9 Unspecified LATE EFFECTS OF INFECTIOUS AND PARASITIC DISEASES (137-139) 137 Late effects of tuberculosis Note: This category is to be used to indicate conditions in 010-018 as the cause of late effects, which are themselves classified elsewhere. The "late effects" include those specified as such, as sequelae, or as due to old or inactive tuberculosis, without evidence of active disease. 137.0 Late effects of respiratory or unspecified tuberculosis 137.1 Late effects of central nervous system tuberculosis 137.2 Late effects of genitourinary tuberculosis 137.3 Late effects of tuberculosis of bones and joints 137.4 Late effects of tuberculosis of other specified organs 138 Late effects of acute poliomyelitis Note: This category is to be used to indicate conditions in to 045.- as the cause of late effects, which are themselves classified elsewhere. The "late effects" include conditions specified as such, or as sequelae, or those which are present one year or more after the onset of the acute poliomyelitis. 139 Late effects of other infectious and parasitic diseases Note: This category is to be used to indicate conditions in categories 001-009, 020-041, 046-136 as the cause of late effects, which are themselves classified elsewhere. The "late effects" include conditions specified as such; they also include sequela of diseases classifiable to the above categories if there is evidence that the disease itself is no longer present. 139.0 Late effects of viral encephalitis Late effects of conditions classifiable to 049.8, 049.9, 062-064 139.1 Late effects of trachoma Late effects of conditions classifiable to 076.- 139.8 Late effects of other and unspecified infectious and parasitic diseases II. NEOPLASMS Notes: 1. Content: This chapter contains the following broad groups:-- 140-195 Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphatic and hematopoietic tissue 196-198 Malignant neoplasms, stated or presumed to be secondary, of specified sites 199 Malignant neoplasms without specification of site 200-208 Malignant neoplasms, stated or presumed to be primary, of lymphatic and hematopoietic tissue 210-229 Benign neoplasms 230-234 Carcinoma in situ 235-238 Neoplasms of uncertain behavior [see Note, page 140] 239 Neoplasms of unspecified nature 2. Functional activity All neoplasms are classified in this chapter, whether or not functionally active. 3. Malignant neoplasms overlapping site boundaries Categories 140-195 are for the classification of primary malignant neoplasms according to their point of origin. A malignant neoplasm that overlaps two or more subcategories within a three-digit rubric and whose point of origin cannot be determined should be classified to the subcategory .8 "Other." For example: "carcinoma involving tip and ventral surface of tongue" should be assigned to 141.8. On the other hand, "carcinoma of tip of tongue extending to involve the ventral surface" should be coded to 141.2 as the point of origin, the tip, is known. Three subcategories (149.8, 159.8, 165.8) have been provided for malignant neoplasms that overlap the boundaries of three-digit rubrics within certain systems. Overlapping malignant neoplasms that cannot be classified as indicated above should be assigned to the appropriate subdivision of category 195 (Malignant neoplasm of other and ill-defined sites). MALIGNANT NEOPLASM OF LIP, ORAL CAVITY, AND PHARYNX (140-149) 140 Malignant neoplasm of lip Excludes: skin of lip (173.0) 140.0 Upper lip, vermilion border Upper lip: NOS external lipstick area 140.1 Lower lip, vermilion border Lower lip: NOS external lipstick area 140.3 Upper lip, inner aspect Upper lip: buccal aspect frenulum mucosa oral aspect 140.4 Lower lip, inner aspect Lower lip: buccal aspect frenulum mucosa oral aspect 140.5 Lip, unspecified, inner aspect Lip, not specified whether upper or lower: buccal aspect frenulum mucosa oral aspect 140.6 Commissure of lip 140.8 Other [see Note 3 at beginning of Chapter II] 140.9 Lip, unspecified, vermilion border Lip, not specified as upper or lower: NOS external lipstick area 141 Malignant neoplasm of tongue 141.0 Base of tongue Dorsal surface of base of tongue Fixed part of tongue NOS 141.1 Dorsal surface of tongue Anterior two-thirds of tongue, dorsal surface Excludes: dorsal surface of base of tongue (141.0) 141.2 Tip and lateral border of tongue 141.3 Ventral surface of tongue Anterior two-thirds of tongue, ventral surface Frenulum linguae 141.4 Anterior two-thirds of tongue, part unspecified Mobile part of tongue NOS 141.5 Junctional zone Border of tongue at junction of fixed and mobile parts at insertion of anterior tonsillar pillar 141.6 Lingual tonsil 141.8 Other [see Note 3 at beginning of Chapter II] 141.9 Tongue, unspecified Tongue NOS 142 Malignant neoplasm of major salivary glands Excludes: malignant neoplasm of minor salivary glands, which are to be classified according to their anatomical location; if location is not specified, classify to 145.9. 142.0 Parotid gland 142.1 Submandibular gland Submaxillary gland 142.2 Sublingual gland 142.8 Other [see Note 3 at beginning of Chapter II] 142.9 Site unspecified Salivary gland (major) NOS 143 Malignant neoplasm of gum Includes: alveolar (ridge) mucosa gingiva Excludes: malignant odontogenic neoplasms (170.-) 143.0 Upper gum 143.1 Lower gum 143.8 Other [see Note 3 at beginning of Chapter II] 143.9 Gum, unspecified 144 Malignant neoplasm of floor of mouth 144.0 Anterior portion Anterior to the premolar-canine junction 144.1 Lateral portion 144.8 Other [see Note 3 at beginning of Chapter II] 144.9 Part unspecified 145 Malignant neoplasm of other and unspecified parts of mouth Excludes: mucosa of lips (140.-) 145.0 Cheek mucosa Buccal mucosa Internal cheek 145.1 Vestibule of mouth Buccal sulcus (upper) (lower) Labial sulcus (upper) (lower) 145.2 Hard palate 145.3 Soft palate Excludes: nasopharyngeal [posterior] [superior] surface of soft palate (147.3) 145.4 Uvula 145.5 Palate, unspecified Junction of hard and soft palate Roof of mouth 145.6 Retromolar area 145.8 Other [see Note 3 at beginning of Chapter II] 145.9 Mouth, unspecified Minor salivary gland, unspecified site Oral cavity NOS 146 Malignant neoplasm of oropharynx 146.0 Tonsil Tonsil: NOS faucial palatine Excludes: lingual tonsil (141.6) pharyngeal tonsil (147.1) 146.1 Tonsillar fossa 146.2 Tonsillar pillars (anterior) (posterior) Palatoglossal arch Palatopharyngeal arch 146.3 Vallecula Anterior and medial surface of the pharyngoepiglottic fold 146.4 Anterior aspect of epiglottis Epiglottis, free border [margin] Glossoepiglottic fold(s) Excludes: epiglottis: NOS (161.1) suprahyoid portion (161.1) 146.5 Junctional region Junction of the free margin of the epiglottis, the aryepiglottic fold, and the pharyngoepiglottic fold 146.6 Lateral wall of oropharynx 146.7 Posterior wall of oropharynx 146.8 Other [see Note 3 at beginning of Chapter II] 146.9 Oropharynx, unspecified 147 Malignant neoplasm of nasopharynx 147.0 Superior wall Roof of nasopharynx 147.1 Posterior wall Adenoid Pharyngeal tonsil 147.2 Lateral wall Fossa of Rosenmller Pharyngeal recess Opening of auditory tube 147.3 Anterior wall Floor of nasopharynx Nasopharyngeal [posterior] [superior] surface of soft palate Posterior margin of nasal septum and choanae 147.8 Other [see Note 3 at beginning of Chapter II] 147.9 Nasopharynx, unspecified Nasopharyngeal wall NOS 148 Malignant neoplasm of hypopharynx 148.0 Postcricoid region 148.1 Pyriform sinus Pyriform fossa 148.2 Aryepiglottic fold, hypopharyngeal aspect Aryepiglottic fold or interarytenoid fold: NOS marginal zone Excludes: aryepiglottic fold or interarytenoid fold, laryngeal aspect (161.1) 148.3 Posterior hypopharyngeal wall 148.8 Other [see Note 3 at beginning of Chapter II] 148.9 Hypopharynx, unspecified Hypopharyngeal wall NOS Hypopharynx NOS 149 Malignant neoplasm of other and ill-defined sites within the lip, oral cavity, and pharynx 149.0 Pharynx, unspecified 149.1 Waldeyer's ring 149.8 Other [see Note 3 at beginning of Chapter II] Malignant neoplasms of lip, oral cavity, and pharynx whose point of origin cannot be assigned to any one of the categories 140-148 149.9 Ill-defined MALIGNANT NEOPLASM OF DIGESTIVE ORGANS AND PERITONEUM (150-159) 150 Malignant neoplasm of esophagus Note: Two alternative subclassifications are given:-- .0-.2 by anatomical description .3-.5 by thirds This departure from the principle that categories should be mutually exclusive is deliberate, since both forms of terminology are currently encountered on medical records. 150.0 Cervical part 150.1 Thoracic part 150.2 Abdominal part 150.3 Upper third 150.4 Middle third 150.5 Lower third 150.8 Other [see Note 3 at beginning of Chapter II] 150.9 Esophagus, unspecified 151 Malignant neoplasm of stomach 151.0 Cardia Cardiac orifice Cardio-esophageal junction 151.1 Pylorus Prepylorus Pyloric canal 151.2 Pyloric antrum Antrum of stomach NOS 151.3 Fundus of stomach 151.4 Body of stomach 151.5 Lesser curvature, unspecified Lesser curvature, not classifiable to 151.1-151.4 151.6 Greater curvature, unspecified Greater curvature, not classifiable to 151.0-151.4 151.8 Other [see Note 3 at beginning of Chapter II] Anterior wall, not classifiable to 151.0-151.4 Posterior wall, not classifiable to 151.0-151.4 151.9 Stomach, unspecified Carcinoma ventriculi Gastric cancer 152 Malignant neoplasm of small intestine, including duodenum 152.0 Duodenum 152.1 Jejunum 152.2 Ileum Excludes: ileocaecal valve (153.4) 152.3 Meckel's diverticulum 152.8 Other [see Note 3 at beginning of Chapter II] Duodenojejunal junction 152.9 Small intestine, unspecified 153 Malignant neoplasm of colon 153.0 Hepatic flexure 153.1 Transverse colon 153.2 Descending colon 153.3 Sigmoid colon Sigmoid (flexure) Excludes: rectosigmoid junction (154.0) 153.4 Caecum Ileocecal valve 153.5 Appendix 153.6 Ascending colon 153.7 Splenic flexure 153.8 Other [see Note 3 at beginning of Chapter II] 153.9 Colon, unspecified Large intestine NOS 154 Malignant neoplasm of rectum, rectosigmoid junction, and anus 154.0 Rectosigmoid junction Colon and rectum Rectosigmoid (colon) 154.1 Rectum Rectal ampulla 154.2 Anal canal Anal sphincter 154.3 Anus, unspecified Excludes: anus: margin (172.5, 173.5) skin (172.5, 173.5) perianal skin (172.5, 173.5) 154.8 Other [see Note 3 at beginning of Chapter II] Anorectum Cloacogenic zone 155 Malignant neoplasm of liver and intrahepatic bile ducts 155.0 Liver, primary Carcinoma: liver, specified as primary hepatocellular liver cell Hepatoblastoma 155.1 Intrahepatic bile ducts Canaliculi biliferi Intrahepatic: Interlobular: biliary passages bile ducts canaliculi biliary canals gall duct 155.2 Liver, not specified as primary or secondary 156 Malignant neoplasm of gallbladder and extrahepatic bile ducts 156.0 Gallbladder 156.1 Extrahepatic bile ducts Biliary duct or passage NOS Cystic duct Common bile duct Hepatic duct 156.2 Ampulla of Vater 156.8 Other [see Note 3 at beginning of Chapter II] 156.9 Biliary tract, part unspecified Malignant neoplasm involving both intrahepatic and extrahepatic bile ducts 157 Malignant neoplasm of pancreas 157.0 Head of pancreas 157.1 Body of pancreas 157.2 Tail of pancreas 157.3 Pancreatic duct Duct of: Santorini Wirsung 157.4 Islets of Langerhans Islets of Langerhans, any part of pancreas 157.8 Other [see Note 3 at beginning of Chapter II] 157.9 Part unspecified 158 Malignant neoplasm of retroperitoneum and peritoneum 158.0 Retroperitoneum 158.8 Specified parts of peritoneum [see Note 3 at beginning of Chapter II] Mesentery Peritoneum: Mesocolon parietal Omentum pelvic 158.9 Peritoneum, unspecified 159 Malignant neoplasm of other and ill-defined sites within the digestive organs and peritoneum 159.0 Intestinal tract, part unspecified Intestine NOS 159.1 Spleen, not elsewhere classified Angiosarcoma of spleen Fibrosarcoma of spleen Excludes: Hodgkin's disease (201.-) lymphosarcoma (200.1) reticulosarcoma (200.0) 159.8 Other [see Note 3 at beginning of Chapter II] Malignant neoplasm of digestive organs and peritoneum whose point of origin cannot be assigned to any one of the categories 150-158 Excludes: cardio-esophageal junction (151.0) colon and rectum (154.0) 159.9 Ill-defined Alimentary canal or tract NOS Gastrointestinal tract NOS MALIGNANT NEOPLASM OF RESPIRATORY AND INTRATHORACIC ORGANS (160-165) 160 Malignant neoplasm of nasal cavities, middle ear, and accessory sinuses 160.0 Nasal cavities Cartilage of nose Septum of nose Conchae, nasal Vestibule of nose Internal nose Excludes: nasal bone (170.0) nose NOS (195.0) olfactory bulb (192.0) posterior margin of septum and choanae (147.3) skin of nose (172.3, 173.3) 160.1 Auditory tube, middle ear, and mastoid air cells Antrum tympanicum Tympanic cavity Eustachian tube Excludes: auricular canal (external) (172.2, 173.2) bone of ear (meatus) (170.0) cartilage of ear (171.0) ear (external) (skin) (172.2, 173.2) 160.2 Maxillary sinus Antrum (Highmore) (maxillary) 160.3 Ethmoidal sinus 160.4 Frontal sinus 160.5 Sphenoidal sinus 160.8 Other [see Note 3 at beginning of Chapter II] 160.9 Accessory sinus, unspecified 161 Malignant neoplasm of larynx 161.0 Glottis Intrinsic larynx True vocal cord Laryngeal commissure Vocal cord NOS (anterior) (posterior) 161.1 Supraglottis Aryepiglottic fold or interarytenoid fold, laryngeal aspect Epiglottis (suprahyoid portion) NOS Extrinsic larynx False vocal cords Posterior (laryngeal) surface of epiglottis Ventricular bands Excludes: anterior aspect of epiglottis (146.4) aryepiglottic fold or interarytenoid fold: NOS (148.2) hypopharyngeal aspect (148.2) marginal zone (148.2) 161.2 Subglottis 161.3 Laryngeal cartilages Cartilage: Cartilage: arytenoid cuneiform cricoid thyroid 161.8 Other [see Note 3 at beginning of Chapter II] 161.9 Larynx, unspecified 162 Malignant neoplasm of trachea, bronchus, and lung 162.0 Trachea 162.2 Main bronchus Carina Hilus 162.3 Upper lobe, bronchus or lung 162.4 Middle lobe, bronchus or lung 162.5 Lower lobe, bronchus or lung 162.8 Other [see Note 3 at beginning of Chapter II] 162.9 Bronchus and lung, unspecified 163 Malignant neoplasm of pleura 163.0 Parietal 163.1 Visceral 163.8 Other [see Note 3 at beginning of Chapter II] 163.9 Pleura, unspecified 164 Malignant neoplasm of thymus, heart, and mediastinum 164.0 Thymus 164.1 Heart Pericardium Excludes: great vessels (171.4) 164.2 Anterior mediastinum 164.3 Posterior mediastinum 164.8 Other [see Note 3 at beginning of Chapter II] 164.9 Mediastinum, part unspecified 165 Malignant neoplasm of other and ill-defined sites within the respiratory system and intrathoracic organs 165.0 Upper respiratory tract, part unspecified 165.8 Other [see Note 3 at beginning of Chapter II] Malignant neoplasms of respiratory and intrathoracic organs whose point of origin cannot be assigned to any one of the categories 160-164 165.9 Ill-defined sites within the respiratory system Respiratory tract NOS Excludes: intrathoracic NOS (195.1) thoracic NOS (195.1) MALIGNANT NEOPLASM OF BONE, CONNECTIVE TISSUE, SKIN, AND BREAST (170-175) 170 Malignant neoplasm of bone and articular cartilage Excludes: bone marrow NOS (202.9) cartilage: ear (171.0) eyelid (171.0) larynx (161.3) nose (160.0) synovia (171.-) 170.0 Bones of skull and face Bone: Bone: ethmoid sphenoid frontal temporal malar zygomatic nasal Maxilla occipital Turbinate orbital Vomer parietal Excludes: carcinoma, any type other than intraosseous or odontogenic: maxilla, maxillary (sinus) (160.2) upper jaw bone (143.0) jaw bone (lower) (170.1) 170.1 Lower jaw bone Mandible Jaw bone NOS Excludes: carcinoma, any type other than intraosseous or odontogenic: jaw bone NOS (143.9) lower (143.1) upper jaw bone (170.0) 170.2 Vertebral column, excluding sacrum and coccyx Spinal column Vertebra Spine 170.3 Ribs, sternum, and clavicle Costal cartilage Xiphoid process 170.4 Long bones of upper limb and scapula Acromion process Radius Bones NOS of upper limb Ulna Humerus 170.5 Upper limbs, Short bones Carpal Scaphoid (of hand) Cuneiform, wrist Semilunar or lunate Metacarpal Trapezium Phalanges of hand Trapezoid Pisiform Unciform 170.6 Pelvic bones, sacrum, and coccyx Coccygeal vertebra Ilium Ischium Pubic bone Sacral vertebra 170.7 Lower limb, long bones Bones NOS of lower limb Femur Fibula Tibia 170.8 Lower limb, short bones Astragalus Navicular (of ankle) Calcaneus Patella Cuboid Phalanges of foot Cuneiform, ankle Tarsal Metatarsal 170.9 Site unspecified Chondrosarcoma } Chondromyxosarcoma } site unspecified Ewing's sarcoma or tumor } Osteosarcoma } 171 Malignant neoplasm of connective and other soft tissue Includes: blood vessel peripheral, sympathetic, and bursa parasympathetic nerves fascia and ganglia fat synovia ligament, except uterine tendon (sheath) muscle Excludes: cartilage (of): articular (170.-) larynx (161.3) nose (160.0) connective tissue of breast (174.-) heart (164.1) 171.0 Head, face, and neck Cartilage of: ear eyelid 171.2 Upper limb, including shoulder 171.3 Lower limb, including hip 171.4 Thorax Axilla Diaphragm Great vessels Excludes: thymus, heart and mediastinum (164.-) 171.5 Abdomen Abdominal wall Hypochondrium 171.6 Pelvis Buttock Groin Perineum Excludes: uterine ligament, any (183.-) 171.7 Trunk, unspecified Back NOS 171.8 Other [see Note 3 at beginning of Chapter II] 171.9 Site unspecified Fibrosarcoma } Hemangiosarcoma } Leiomysarcoma } Liposarcoma } Lymphangiosarcoma } site unspecified Myosarcoma } Myxosarcoma } Rhabdomyosarcoma } Sarcoma } Sarcomatosis } 172 Malignant melanoma of skin Includes: melanocarcinoma melanoma (skin) NOS Excludes: skin of genital organs (184.-) 172.0 Lip Excludes: vermilion border of lip (140.-) 172.1 Eyelid, including canthus 172.2 Ear and external auditory canal Auricle (ear) Pinna External meatus 172.3 Other and unspecified parts of face Cheek (external) Nose, external Eyebrow Temple 172.4 Scalp and neck 172.5 Trunk, except scrotum Axilla Perianal skin Breast Perineum Buttock Umbilicus Groin Excludes: anus NOS (154.3) scrotum (187.7) 172.6 Upper limb, including shoulder 172.7 Lower limb, including hip 172.8 Other [see Note 3 at beginning of Chapter II] 172.9 Site unspecified 173 Other malignant neoplasm of skin Includes: malignant neoplasm of: sebaceous glands sweat glands Excludes: malignant melanoma of skin (172.-) skin of genital organs (184.-, 187.-) 173.0 Skin of lip Excludes: vermilion border of lip (140.-) 173.1 Eyelid, including canthus Excludes: cartilage of eyelid (171.0) 173.2 Ear and external auricular canal Auricle (ear) Pinna External meatus Excludes: cartilage of ear (171.0) 173.3 Skin of other and unspecified parts of face Cheek, external Nose, external Eyebrow Temple 173.4 Scalp and skin of neck 173.5 Skin of trunk, except scrotum Axillary fold Perianal skin Umbilicus Skin of: abdominal wall anus back breast buttock chest wall groin perineum Excludes: anal canal (154.2) anus NOS (154.3) skin of scrotum (187.7) 173.6 Skin of upper limb, including shoulder 173.7 Skin of lower limb, including hip 173.8 Other [see Note 3 at beginning of Chapter II] 173.9 Site unspecified 174 Malignant neoplasm of female breast Includes: breast (female) connective tissue soft parts Paget's disease of: breast nipple Excludes: skin of breast (172.5, 173.5) 174.0 Nipple and areola 174.1 Central portion 174.2 Upper-inner quadrant 174.3 Lower-inner quadrant 174.4 Upper-outer quadrant 174.5 Lower-outer quadrant 174.6 Axillary tail 174.8 Other [see Note 3 at beginning of Chapter II] Ectopic sites 174.9 Breast, unspecified 175 Malignant neoplasm of male breast Excludes: skin of breast (172.5, 173.5) MALIGNANT NEOPLASM OF GENITOURINARY ORGANS (179-189) 179 Malignant neoplasm of uterus, part unspecified 180 Malignant neoplasm of cervix uteri 180.0 Endocervix Cervical canal NOS Endocervical gland Endocervical canal 180.1 Exocervix 180.8 Other [see Note 3 at beginning of Chapter II] 180.9 Cervix uteri, unspecified 181 Malignant neoplasm of placenta Choriocarcinoma NOS Chorioepithelioma NOS Excludes: chorioadenoma (destruens) (236.1) hydatidiform mole (630) malignant (236.1) 182 Malignant neoplasm of body of uterus 182.0 Corpus uteri, except isthmus Cornu Fundus Endometrium Myometrium 182.1 Isthmus Lower uterine segment 182.8 Other [see Note 3 at beginning of Chapter II] 183 Malignant neoplasm of ovary and other uterine adnexa 183.0 Ovary 183.2 Fallopian tube Oviduct Uterine tube 183.3 Broad ligament 183.4 Parametrium Uterine ligament NOS 183.5 Round ligament 183.8 Other [see Note 3 at beginning of Chapter II] 183.9 Uterine adnexa, unspecified 184 Malignant neoplasm of other and unspecified female genital organs 184.0 Vagina 184.1 Labia majora Greater vestibular [Bartholin's] gland 184.2 Labia minora 184.3 Clitoris 184.4 Vulva, unspecified External female genitalia NOS Pudendum 184.8 Other [see Note 3 at beginning of Chapter II] 184.9 Site unspecified Female genitourinary tract NOS 185 Malignant neoplasm of prostate 186 Malignant neoplasm of testis 186.0 Undescended Ectopic testis Retained testis 186.9 Other and unspecified Testis: NOS descended scrotal 187 Malignant neoplasm of penis and other male genital organs 187.1 Prepuce Foreskin 187.2 Glans penis 187.3 Body of penis Corpus cavernosum 187.4 Penis, part unspecified Skin of penis NOS 187.5 Epididymis 187.6 Spermatic cord 187.7 Scrotum Skin of scrotum 187.8 Other [see Note 3 at beginning of Chapter II] 187.9 Site unspecified Male genital organ or tract NOS 188 Malignant neoplasm of bladder 188.0 Trigone 188.1 Dome 188.2 Lateral wall 188.3 Anterior wall 188.4 Posterior wall 188.5 Bladder neck Internal urethral orifice 188.6 Ureteric orifice 188.7 Urachus 188.8 Other [see Note 3 at beginning of Chapter II] 188.9 Part unspecified 189 Malignant neoplasm of kidney and other and unspecified urinary organs 189.0 Kidney, except pelvis 189.1 Renal pelvis Renal calyces Pelviureteric junction 189.2 Ureter Excludes: ureteric orifice of bladder (188.6) 189.3 Urethra Excludes: urethral orifice of bladder (188.5) 189.4 Paraurethral glands 189.8 Other [see Note 3 at beginning of Chapter II] 189.9 Site unspecified Urinary system NOS MALIGNANT NEOPLASM OF OTHER AND UNSPECIFIED SITES (190-199) 190 Malignant neoplasm of eye Excludes: eyelid (skin) (172.1, 173.1) cartilage of eyelid (171.0) optic nerve (192.0) orbital bone (170.0) 190.0 Eyeball, except conjunctiva, cornea, retina, and choroid Ciliary body 190.1 Orbit Connective tissue of orbit Retrobulbar Extraocular muscle Excludes: orbit bone (170.0) 190.2 Lacrimal gland 190.3 Conjunctiva 190.4 Cornea 190.5 Retina 190.6 Choroid 190.7 Lacrimal duct Lacrimal sac Nasolacrimal duct 190.8 Other [see Note 3 at beginning of Chapter II] 190.9 Part unspecified 191 Malignant neoplasm of brain Excludes: cranial nerves (192.-) retrobulbar area (190.1) 191.0 Cerebrum, except lobes and ventricles 191.1 Frontal lobe 191.2 Temporal lobe 191.3 Parietal lobe 191.4 Occipital lobe 191.5 Ventricles Floor of ventricle 191.6 Cerebellum 191.7 Brain stem 191.8 Other [see Note 3 at beginning of Chapter II] 191.9 Brain, unspecified Astrocytoma } Astroblastoma } Ependymoma } site unspecified Glioma } Medulloblastoma } Neuroepithelioma } Oligodendroblastoma } 192 Malignant neoplasm of other and unspecified parts of nervous system Excludes: peripheral, sympathetic, and parasympathetic nerves and ganglia (171.-) 192.0 Cranial nerves 192.1 Cerebral meninges Meninges NOS 192.2 Spinal cord 192.3 Spinal meninges 192.8 Other [see Note 3 at beginning of Chapter II] 192.9 Part unspecified Nervous system (central) NOS Excludes: meninges NOS (192.1) 193 Malignant neoplasm of thyroid gland 194 Malignant neoplasm of other endocrine glands and related structures Excludes: islets of Langerhans (157.4) 194.0 Suprarenal gland Adrenal gland 194.1 Parathyroid gland 194.3 Pituitary gland and craniopharyngeal duct 194.4 Pineal gland 194.5 Carotid body 194.6 Aortic body and other paraganglia 194.8 Other Pluriglandular involvement NOS Note: If the sites of multiple involvements are known, they should be coded separately. 194.9 Site unspecified Endocrine gland NOS 195 Malignant neoplasm of other and ill-defined sites Includes: overlapping neoplasms, not elsewhere classified [see Note 3 at beginning of Chapter II] Excludes: malignant neoplasm: lymphatic and hematopoietic tissue (200-208) unspecified site (199.-) 195.0 Head, face, and neck Cheek NOS Nose NOS 195.1 Thorax Axilla 195.2 Abdomen 195.3 Pelvis Groin Sites overlapping systems within pelvis, such as: rectovaginal (septum) rectovesical (septum) 195.4 Upper limb 195.5 Lower limb 195.8 Other specified sites 196 Secondary and unspecified malignant neoplasm of lymph nodes [Not to be used for underlying cause of death] Excludes: any malignant neoplasm of lymph nodes, specified as primary (200-202) Hodgkin's disease (201.-) lymphosarcoma (200.1) other forms of lymphoma (202.-) reticulosarcoma (200.0) 196.0 Head, face, and neck Cervicofacial Supraclavicular 196.1 Intrathoracic Bronchopulmonary Tracheobronchial Mediastinal 196.2 Intra-abdominal Intestinal Retroperitoneal Mesenteric 196.3 Axilla and upper limb Brachial Pectoral Epitrochlear 196.5 Inguinal and lower limb Groin Tibial Popliteal 196.6 Intrapelvic lymph nodes Iliac Obturator 196.8 Multiple sites 196.9 Site unspecified Lymph nodes NOS 197 Secondary malignant neoplasm of respiratory and digestive systems [Not to be used for underlying cause of death]. 197.0 Lung 197.1 Mediastinum 197.2 Pleura 197.3 Other respiratory organs 197.4 Small intestine, including duodenum 197.5 Large intestine and rectum 197.6 Retroperitoneum and peritoneum 197.7 Liver 197.8 Other digestive organs 198 Secondary malignant neoplasm of other specified sites [Not to be used for underlying cause of death] 198.0 Kidney 198.1 Other urinary organs 198.2 Skin 198.3 Brain and spinal cord 198.4 Other parts of nervous system Meninges (cerebral) (spinal) 198.5 Bone and bone marrow 198.6 Ovary 198.7 Suprarenal gland 198.8 Other specified sites 199 Malignant neoplasm without specification of site 199.0 Disseminated Carcinomatosis unspecified site (primary) (secondary) Generalized: cancer unspecified site (primary) (secondary) malignancy unspecified site (primary) (secondary) Multiple cancer unspecified site (primary) (secondary) 199.1 Other Cancer unspecified site (primary) (secondary) Carcinoma unspecified site (primary) (secondary) Malignancy unspecified site (primary) (secondary) MALIGNANT NEOPLASM OF LYMPHATIC AND HEMATOPOIETIC TISSUE (200-208) Excludes: secondary and unspecified neoplasm of lymph nodes (196.-) 200 Lymphosarcoma and reticulosarcoma 200.0 Reticulosarcoma 200.1 Lymphosarcoma Excludes: lymphosarcoma cell leukemia (207.8) 200.2 Burkitt's tumor 200.8 Other named variants Reticulolymphosarcoma 201 Hodgkin's disease Note: Two alternative sub-classifications are given: .0-.2 Parker-Jackson .4-.7 Rye modification of Lukes-Butler This departure from the principle that categories should be mutually exclusive is deliberate, since both forms of terminology are currently encountered on medical records. 201.0 Hodgkin's paragranuloma 201.1 Hodgkin's granuloma 201.2 Hodgkin's sarcoma 201.4 Lymphocytic-histiocytic predominance 201.5 Nodular sclerosis 201.6 Mixed cellularity 201.7 Lymphocytic depletion 201.9 Unspecified 202 Other malignant neoplasms of lymphoid and histiocytic tissue 202.0 Nodular lymphoma Brill-Symmers disease Follicular lymphoma 202.1 Mycosis fungoides 202.2 S‚zary's disease 202.3 Malignant histiocytosis 202.4 Leukemic reticuloendotheliosis Hairy-cell leukemia 202.5 Letterer-Siwe disease Acute: differentiated progressive histiocytosis progressive histiocytosis X infantile reticuloendotheliosis reticulosis of infancy Excludes: histiocytosis (acute) (chronic) (277.8) histiocytosis X (chronic) (277.8) 202.6 Malignant mast-cell tumors Malignant: Mast-cell sarcoma mastocytoma mastocytosis Excludes: mast-cell leukemia (207.8) 202.8 Other lymphomas Lymphoma (malignant): NOS diffuse 202.9 Other and unspecified 203 Multiple myeloma and immunoproliferative neoplasms 203.0 Multiple myeloma Kahler's disease Myelomatosis Excludes: solitary myeloma (238.6) 203.1 Plasma cell leukemia 203.8 Other immunoproliferative neoplasms 204 Lymphoid leukemia Includes: leukemia: lymphatic lymphocytic 204.0 Acute Excludes: acute exacerbation of chronic lymphoid leukemia (204.1) 204.1 Chronic 204.2 Subacute 204.8 Other 204.9 Unspecified 205 Myeloid leukemia Includes: leukemia: granulocytic myelogenous 205.0 Acute Excludes: acute exacerbation of chronic myeloid leukemia (205.1) 205.1 Chronic 205.2 Subacute 205.3 Myeloid sarcoma Chloroma Granulocytic sarcoma 205.8 Other 205.9 Unspecified 206 Monocytic leukemia Includes: monocytoid leukemia 206.0 Acute Excludes: acute exacerbation of chronic monocytic leukemia (206.1) 206.1 Chronic 206.2 Subacute 206.8 Other 206.9 Unspecified 207 Other specified leukemia Excludes: leukemic reticuloendotheliosis (202.4) plasma cell leukemia (203.1) 207.0 Acute erythremia and erythroleukemia Acute erythremic myelosis Di Guglielmo's disease 207.1 Chronic erythremia Heilmeyer-Sch”ner disease 207.2 Megakaryocytic leukemia 207.8 Other Lymphosarcoma cell leukemia 208 Leukemia of unspecified cell type 208.0 Acute Acute leukemia NOS Stem cell leukemia Blast cell leukemia Excludes: acute exacerbation of unspecified leukemia (208.1) 208.1 Chronic Chronic leukemia NOS 208.2 Subacute Subacute leukemia NOS 208.8 Other 208.9 Unspecified Leukemia NOS BENIGN NEOPLASMS (210-229) 210 Benign neoplasm of lip, oral cavity, and pharynx Excludes: cyst of jaw (522.-, 526.-) cyst of oral soft tissue (528.-) 210.0 Lip Frenulum labii Lip (inner aspect) (mucosa) (vermilion border) Excludes: labial commissure (210.4) skin of lip (216.0) 210.1 Tongue Lingual tonsil 210.2 Major salivary glands Gland: parotid sublingual submandibular Excludes: benign neoplasms of minor salivary glands which are to be classified according to their anatomical location; if location is not specified, classify to 210.4 210.3 Floor of mouth 210.4 Other and unspecified parts of mouth Gingiva Oral mucosa Labial commissure Palate (hard) (soft) Oral cavity NOS Uvula Excludes: benign odontogenic neoplasms (213.-) mucosa of lips (210.0) nasopharyngeal [posterior] [superior] surface of soft palate (210.7) 210.5 Tonsil Tonsil (faucial) (palatine) Excludes: lingual tonsil (210.1) pharyngeal tonsil (210.7) tonsillar: fossa (210.6) pillars (210.6) 210.6 Other parts of oropharynx Epiglottis, anterior aspect Vallecula Tonsillar: fossa pillars Excludes: epiglottis: NOS (212.1) suprahyoid portion (212.1) 210.7 Nasopharynx 210.8 Hypopharynx 210.9 Pharynx, unspecified 211 Benign neoplasm of other parts of digestive system 211.0 Esophagus 211.1 Stomach 211.2 Small intestine, including duodenum Excludes: ampulla of Vater (211.5) ileocecal valve (211.3) 211.3 Colon Excludes: rectosigmoid junction (211.4) 211.4 Rectum and anal canal Anus NOS Excludes: anus: margin (216.5) skin (216.5) perianal skin (216.5) 211.5 Liver and biliary passages 211.6 Pancreas, except islets of Langerhans 211.7 Islets of Langerhans Islet cell tumor 211.8 Retroperitoneum and peritoneum 211.9 Other and unspecified site Alimentary canal or tract NOS Intestine NOS Gastrointestinal tract NOS Spleen, not elsewhere classified 212 Benign neoplasm of respiratory and intrathoracic organs 212.0 Nasal cavities, middle ear, and accessory sinuses Excludes: auricular canal (external) (216.2) bone of: ear (213.0) nose (213.0) cartilage of ear (215.0) ear (external) (skin) (216.2) nose NOS (229.8) skin (216.3) olfactory bulb (225.1) polyp of: accessory sinus (471.8) ear (387.9) nasal cavity (471.0) posterior margin of septum and choanae (210.7) 212.1 Larynx Excludes: epiglottis, anterior aspect (210.6) polyp of vocal cord or larynx (478.4) 212.2 Trachea 212.3 Bronchus and lung 212.4 Pleura 212.5 Mediastinum 212.6 Thymus 212.7 Heart Excludes: great vessels (215.4) 212.8 Other specified sites 212.9 Site unspecified Respiratory organ NOS Upper respiratory tract NOS Excludes: intrathoracic NOS (229.8) thoracic NOS (229.8) 213 Benign neoplasm of bone and articular cartilage Excludes: cartilage of: ear (215.0) eyelid (215.0) larynx (212.1) nose (212.0) synovia (215.-) 213.0 Bones of skull and face Excludes: lower jaw bone (213.1) 213.1 Lower jaw bone 213.2 Vertebral column, excluding sacrum and coccyx 213.3 Ribs, sternum, and clavicle 213.4 Long bones of upper limb and scapula 213.5 Upper limb, short bones 213.6 Pelvic bones, sacrum, and coccyx 213.7 Lower limb, long bones 213.8 Lower limb, short bones 213.9 Site unspecified Chondroma } site Osteoma } unspecified 214 Lipoma Any site: Angiolipoma Fibrolipoma Hibernoma Lipoma (fetal) (infiltrating) (intramuscular) Myxolipoma 215 Other benign neoplasm of connective and other soft tissue Includes: blood vessel peripheral, sympathetic, and bursa parasympathetic nerves and ganglia fascia synovia ligament tendon (sheath) muscle Excludes: cartilage: articular (213.-) larynx (212.1) nose (212.0) connective tissue of breast (217) 215.0 Head, face, and neck 215.2 Upper limb, including shoulder 215.3 Lower limb, including hip 215.4 Thorax Excludes: heart (212.7) mediastinum (212.5) thymus (212.6) 215.5 Abdomen 215.6 Pelvis Excludes: uterine: leiomyoma (218) ligament, any (221.0) 215.7 Trunk, unspecified Back NOS 215.8 Other specified sites 215.9 Site unspecified Leiomyoma } Myoma } site Myxofibroma } unspecified Myxoma } Rhabdomyoma } 216 Benign neoplasm of skin Includes: blue naevus dermatofibroma hydrocystoma pigmented naevus syringoadenoma syringoma Excludes: skin of genital organs (221.-, 222.-) 216.0 Skin of lip Excludes: vermilion border of lip (210.0) 216.1 Eyelid, including canthus Excludes: cartilage of eyelid (215.0) 216.2 Ear and external auditory canal Auricle (ear) Pinna External meatus Excludes: cartilage of ear (215.0) 216.3 Skin of other and unspecified parts of face Cheek, external Nose, external Eyebrow Temple 216.4 Scalp and skin of neck 216.5 Skin of trunk, except scrotum Axillary fold Skin of: Perianal skin abdominal wall Umbilicus anus back breast buttock chest wall groin perineum Excludes: anal canal (211.4) anus NOS (211.4) skin of scrotum (222.4) 216.6 Skin of upper limb, including shoulder 216.7 Skin of lower limb, including hip 216.8 Other 216.9 Site unspecified 217 Benign neoplasm of breast Breast (male) (female) connective tissue soft parts Excludes: benign cyst of breast (610.-) skin of breast (216.5) 218 Uterine leiomyoma Fibroid (uterus) Fibromyoma } uterus Myoma } 219 Other benign neoplasm of uterus 219.0 Cervix uteri 219.1 Corpus uteri 219.8 Other specified parts 219.9 Part unspecified 220 Benign neoplasm of ovary 221 Benign neoplasm of other female genital organs Includes: adenomatous polyp benign teratoma 221.0 Uterine tube and ligaments Fallopian tube Oviduct Uterine ligament (broad) (round) 221.1 Vagina 221.2 Vulva Clitoris External female genitalia NOS Greater vestibular [Bartholin's] gland Labia (majora) (minora) Pudendum 221.8 Other specified sites 221.9 Site unspecified 222 Benign neoplasm of male genital organs 222.0 Testis 222.1 Penis Corpus cavernosum Glans penis Prepuce 222.2 Prostate Excludes: adenomatous hyperplasia of prostate (600) prostatic: adenoma (600) enlargement (600) hypertrophy (600) 222.3 Epididymis 222.4 Scrotum Skin of scrotum 222.8 Other specified sites Seminal vesicle Spermatic cord 222.9 Site unspecified 223 Benign neoplasm of kidney and other urinary organs 223.0 Kidney, except pelvis Excludes: renal: calyces (223.1) pelvis (223.1) 223.1 Renal pelvis 223.2 Ureter Excludes: ureteric orifice of bladder (223.3) 223.3 Bladder 223.8 Other specified sites Paraurethral glands Urethra Excludes: urethral orifice of bladder(223.3) 223.9 Site unspecified Urinary system NOS 224 Benign neoplasm of eye Excludes: cartilage of eyelid (215.0) eyelid (skin) (216.1) optic nerve (225.1) orbital bone (213.0) 224.0 Eyeball, except conjunctiva, cornea, retina, and choroid 224.1 Orbit 224.2 Lacrimal gland 224.3 Conjunctiva 224.4 Cornea 224.5 Retina Excludes: haemangioma of retina (228.0) 224.6 Choroid 224.7 Lacrimal duct Lacrimal sac Nasolacrimal duct 224.8 Other specified parts 224.9 Part unspecified 225 Benign neoplasm of brain and other parts of nervous system Excludes: haemangioma (228.0) peripheral, sympathetic, and parasympathetic nerves and ganglia (215.-) retrobulbar (224.1) 225.0 Brain 225.1 Cranial nerves 225.2 Cerebral meninges Meninges NOS Meningioma (cerebral) 225.3 Spinal cord 225.4 Spinal meninges Spinal meningioma 225.8 Other 225.9 Part unspecified Nervous system (central) NOS Excludes: meninges NOS (225.2) 226 Benign neoplasm of thyroid glands 227 Benign neoplasm of other endocrine glands and related structures 227.0 Suprarenal gland Adrenal gland 227.1 Parathyroid gland 227.3 Pituitary gland and craniopharyngeal duct 227.4 Pineal gland 227.5 Carotid body 227.6 Aortic body and other paraganglia 227.8 Other 227.9 Site unspecified Endocrine gland NOS 228 Hemangioma and lymphangioma, any site Excludes: blue or pigmented naevus (216.-) 228.0 Haemangioma, any site Angioma (benign) (cavernous) (congenital) NOS Glomus tumor Haemangioma (benign) (congenital) Naevus: NOS cavernous vascular Systemic angiomatosis 228.1 Lymphangioma, any site Congenital lymphangioma Lymphatic nevus 229 Benign neoplasm of other and unspecified sites 229.0 Lymph nodes 229.8 Other specified sites 229.9 Site unspecified CARCINOMA IN SITU (230-234) Includes: Bowen's disease erythroplasia Queyrat's erythroplasia 230 Carcinoma in situ of digestive organs 230.0 Lip, oral cavity, and pharynx Gingiva Oropharynx Hypopharynx Salivary gland or duct Mouth [any part] Tongue Nasopharynx Excludes: aryepiglottic fold or interarytenoid fold, laryngeal aspect (231.0) epiglottis: NOS (231.0) suprahyoid portion (231.0) skin of lip (232.0) 230.1 Esophagus 230.2 Stomach 230.3 Colon Excludes: rectosigmoid junction (230.4) 230.4 Rectum 230.5 Anal canal 230.6 Anus, unspecified Excludes: anus: margin (232.5) skin (232.5) perianal skin (232.5) 230.7 Other and unspecified parts of intestine Excludes: ampulla of Vater (230.8) 230.8 Liver and biliary system 230.9 Other and unspecified digestive organs Digestive organ NOS Pancreas 231 Carcinoma in situ of respiratory system 231.0 Larynx Excludes: aryepiglottic fold or interarytenoid fold: NOS (230.0) hypopharyngeal aspect (230.0) marginal zone (230.0) 231.1 Trachea 231.2 Bronchus and lung 231.8 Other specified parts Accessory sinuses Nasal cavities Middle ear Excludes: ear (external) (skin) (232.2) nose NOS (234.8) skin (232.3) 231.9 Part unspecified Respiratory organ NOS 232 Carcinoma in situ of skin Includes: pigment cells 232.0 Skin of lip Excludes: vermilion border of lip (230.0) 232.1 Eyelid, including canthus 232.2 Ear and external auditory canal 232.3 Skin of other and unspecified parts of face 232.4 Scalp and skin of neck 232.5 Skin of trunk, except scrotum Anus, margin Skin of: Axillary fold abdominal wall Perianal skin anus Umbilicus back breast buttock chest wall groin perineum Excludes: anal canal (230.5) anus NOS (230.6) skin of genital organs (233.3, 233.5, 233.6) 232.6 Skin of upper limb, including shoulder 232.7 Skin of lower limb, including hip 232.8 Other specified sites 232.9 Site unspecified 233 Carcinoma in situ of breast and genitourinary system 233.0 Breast Excludes: skin of breast (232.5) 233.1 Cervix uteri 233.2 Other and unspecified parts of uterus 233.3 Other and unspecified female genital organs 233.4 Prostate 233.5 Penis 233.6 Other and unspecified male genital organs 233.7 Bladder 233.9 Other and unspecified urinary organs 234 Carcinoma in situ of other and unspecified sites 234.0 Eye Excludes: eyelid (skin) (232.1) 234.8 Other specified sites Endocrine gland [any] 234.9 Site unspecified Carcinoma in situ NOS NEOPLASMS OF UNCERTAIN BEHAVIOR (235-238) Note: Categories 235-238 classify by site certain histo-morphologically well-defined neoplasms the subsequent behavior of which cannot be predicted from the present appearance. 235 Neoplasm of uncertain behavior of digestive and respiratory systems 235.0 Major salivary glands Gland: parotid sublingual submandibular 235.1 Lip, oral cavity, and pharynx Gingiva Nasopharynx Hypopharynx Oropharynx Mouth Tongue Excludes: aryepiglottic fold or interarytenoid fold, laryngeal aspect (235.6) epiglottis: NOS (235.6) suprahyoid portion (235.6) skin of lip (238.2) 235.2 Stomach, intestines, and rectum 235.3 Liver and biliary passages Ampulla of Vater Gallbladder Bile ducts [any] Liver 235.4 Retroperitoneum and peritoneum 235.5 Other and unspecified digestive organs Anal: canal sphincter Anus NOS Esophagus Pancreas Excludes: anus: margin (238.2) skin (238.2) perianal skin (238.2) 235.6 Larynx Excludes: aryepiglottic fold or interarytenoid fold: NOS (235.1) hypopharyngeal aspect (235.1) marginal zone (235.1) 235.7 Trachea, bronchus, and lung 235.8 Pleura, thymus, and mediastinum 235.9 Other and unspecified respiratory organs Accessory sinuses Nasal cavities Middle ear Respiratory organ NOS Excludes: ear (external) (skin) (238.2) nose (238.8) skin (238.2) 236 Neoplasm of uncertain behavior of genitourinary organs 236.0 Uterus 236.1 Placenta Chorioadenoma (destruens) Malignant hydatid(iform) mole 236.2 Ovary 236.3 Other and unspecified female genital organs 236.4 Testis 236.5 Prostate 236.6 Other and unspecified male genital organs 236.7 Bladder 236.9 Other and unspecified urinary organs Kidney Urethra Ureter 237 Neoplasm of uncertain behavior of endocrine glands and nervous system 237.0 Pituitary gland and craniopharyngeal duct 237.1 Pineal gland 237.2 Suprarenal gland Adrenal gland 237.3 Paraganglia 237.4 Other and unspecified endocrine glands Parathyroid gland Thyroid gland 237.5 Brain and spinal cord 237.6 Meninges Meninges: NOS cerebral spinal 237.7 Neurofibromatosis von Recklinghausen's disease 237.9 Other and unspecified parts of nervous system Cranial nerves 238 Neoplasm of uncertain behavior of other and unspecified sites and tissues 238.0 Bone and articular cartilage Excludes: cartilage: ear (238.1) eyelid (238.1) larynx (235.6) nose (235.9) synovia (238.1) 238.1 Connective and other soft tissue Excludes: cartilage (of): articular (238.0) larynx (235.6) nose (235.9) connective tissue of breast (238.3) 238.2 Skin Excludes: anus NOS (235.5) skin of genital organs (236.3, 236.6) vermilion border of lip (235.1) 238.3 Breast Excludes: skin of breast (238.2) 238.4 Polycythemia vera 238.5 Histiocytic and mast cells Mast cell tumor NOS Mastocytoma NOS 238.6 Plasma cells Plasmacytoma NOS Solitary myeloma 238.7 Other lymphatic and hematopoietic tissues Disease: lymphoproliferative (chronic) NOS myeloproliferative (chronic) NOS Idiopathic thrombocythemia Megakaryocytic myelosclerosis Myelosclerosis with myeloid metaplasia Panmyelosis (acute) Excludes: myelofibrosis (298.8) myelosclerosis NOS (289.8) myelosis: NOS (205.9) megakaryocytic (207.2) 238.8 Other specified sites Eye Heart Excludes: eyelid (skin) (238.2) cartilage (238.1) 238.9 Site unspecified NEOPLASMS OF UNSPECIFIED NATURE (239) Note: Category 239 classifies by site neoplasms of unspecified morphology and behavior. 239 Neoplasms of unspecified nature Includes: "growth" NOS neoplasm NOS new growth NOS tumor NOS 239.0 Digestive system Excludes: anus: margin (239.2) skin (239.2) perianal skin (239.2) 239.1 Respiratory system 239.2 Bone, soft tissue, and skin Excludes: anal canal (239.0) anus NOS (239.0) cartilage: larynx (239.1) nose (239.1) connective tissue of breast (239.3) skin of genital organs (239.5) vermilion border of lip (239.8) 239.3 Breast Excludes: skin of breast (239.2) 239.4 Bladder 239.5 Other genitourinary organs 239.6 Brain Excludes: cerebral meninges (239.7) cranial nerves (239.7) 239.7 Endocrine glands and other parts of nervous system Excludes: peripheral, sympathetic, and parasympathetic nerves and ganglia (239.2) 239.8 Other specified sites Excludes: eyelid (skin) (239.2) cartilage (239.2) great vessels (239.2) optic nerve (239.7) 239.9 Site unspecified III. ENDOCRINE, NUTRITIONAL AND METABOLIC DISEASES, AND IMMUNITY DISORDERS Excludes: endocrine and metabolic disturbances specific to the fetus and newborn (775.-) Note: All neoplasms, whether functionally active or not, are classified in Chapter 2. Codes in Chapter 3 (i.e., 242.8, 246.0, 251-253, 255-259) may be used, if desired, to identify such functional activity associated with any neoplasm, or by ectopic endocrine tissue. DISORDERS OF THYROID GLAND (240-246) 240 Simple and unspecified goiter 240.0 Goiter, specified as simple Includes: conditions in 240.9, specified as simple 240.9 Goiter, unspecified Enlargement of thyroid Goiter or struma: NOS diffuse colloid endemic hyperplastic parenchymatous Excludes: congenital (dyshormonogenic) goiter (246.1) 241 Nontoxic nodular goiter Excludes: adenoma of thyroid (226) cystadenoma of thyroid (226) 241.0 Nontoxic uninodular goiter Thyroid nodule Uninodular goiter (nontoxic) 241.1 Nontoxic multinodular goiter Multinodular goiter (nontoxic) 241.9 Unspecified Adenomatous goiter Struma nodosa (simplex) Nodular goiter (nontoxic) NOS 242 Thyrotoxicosis with or without goiter Excludes: neonatal thyrotoxicosis (775.3) 242.0 Toxic diffuse goiter Exophthalmic or toxic goiter NOS 242.1 Toxic uninodular goiter Thyroid nodule, toxic or with hyperthyroidism Uninodular goiter, toxic or with hyperthyroidism 242.2 Toxic multinodular goiter 242.3 Toxic nodular goiter, unspecified Any condition in 241.9 specified as toxic or with hyperthyroidism 242.4 Thyrotoxicosis from ectopic thyroid nodule 242.8 Thyrotoxicosis of other specified origin Overproduction of thyroid-stimulating hormone Thyrotoxicosis: factitia from ingestion of excessive thyroid material Use additional E code, if desired, to identify cause, if drug-induced 242.9 Thyrotoxicosis without mention of goiter or other cause Hyperthyroidism NOS 243 Congenital hypothyroidism Congenital thyroid insufficiency Cretinism Use additional code, if desired, to identify associated mental retardation Excludes: congenital (dyshormonogenic) goiter (246.1) 244 Acquired hypothyroidism [Not to be used for underlying cause of death] Includes: hypothyroidism (acquired) myxedema (adult) (juvenile) 244.0 Postsurgical hypothyroidism 244.1 Other postablative hypothyroidism Hypothyroidism following therapy, such as irradiation 244.2 Iodine hypothyroidism Hypothyroidism resulting from administration or ingestion of iodide Use additional E code, if desired, to identify drug 244.3 Other iatrogenic hypothyroidism Hypothyroidism resulting from: P-aminosalicylic acid [PAS] Phenylbutazone Resorcinol Use additional E code, if desired, to identify drug 244.8 Other 244.9 Unspecified hypothyroidism Hypothyroidism, primary or NOS Myxedema, primary or NOS 245 Thyroiditis 245.0 Acute thyroiditis Abscess of thyroid Thyroiditis: pyogenic suppurative Use additional code, if desired, to identify organism 245.1 Subacute thyroiditis Thyroiditis: de Quervain's giant-cell granulomatous 245.2 Chronic lymphocytic thyroiditis Autoimmune thyroiditis Lymphocytic thyroiditis (chronic) Hashimoto's disease Struma lymphomatosa 245.3 Chronic fibrous thyroiditis Thyroiditis: ligneous Riedel's 245.4 Iatrogenic thyroiditis Use additional code, if desired, to identify cause 245.8 Other and unspecified chronic thyroiditis Chronic thyroiditis NOS 245.9 Unspecified Thyroiditis NOS 246 Other disorders of thyroid 246.0 Disorders of thyrocalcitonin secretion Hypersecretion of calcitonin or thyrocalcitonin 246.1 Dyshormonogenic goiter Congenital goiter Goiter due to enzyme defect in synthesis of thyroid hormone 246.2 Cyst of thyroid Excludes: cystadenoma (226) 246.3 Hemorrhage and infarction of thyroid 246.8 Other Abnormality of thyroid-binding globulin Atrophy of thyroid 246.9 Unspecified DISEASES OF OTHER ENDOCRINE GLANDS (250-259) 250 Diabetes mellitus Excludes: neonatal diabetes mellitus (775.1) nonclinical diabetes (790.2) when complicating pregnancy, childbirth, or the puerperium (648.0) 250.0 Diabetes mellitus without mention of complication Diabetes mellitus without mention of complication or manifestation classifiable to 250.1-250.9 Diabetes (mellitus) NOS 250.1 Diabetes with ketoacidosis Diabetic: acidosis without mention of coma ketosis without mention of coma 250.2 Diabetes with coma Diabetic coma (with ketoacidosis) Diabetes with hyperosmolar coma 250.3 Diabetes with renal manifestations Diabetic nephropathy Intercapillary glomerulosclerosis Kimmelstiel-Wilson syndrome 250.4 Diabetes with ophthalmic manifestations Diabetic: cataract retinopathy 250.5 Diabetes with neurological manifestations Diabetic: Diabetic polyneuropathy amyotrophy mononeuropathy 250.6 Diabetes with peripheral circulatory disorders Diabetic: gangrene peripheral angiopathy 250.7 Diabetes with other specified manifestations Excludes: intercurrent infections in diabetic patients 250.9 Diabetes with unspecified complications 251 Other disorders of pancreatic internal secretion 251.0 Hypoglycemic coma Iatrogenic hyperinsulinism Insulin coma Use additional E code, if desired, to identify cause, if drug-induced 251.1 Other hyperinsulinism Hyperinsulinism: Hyperplasia of pancreatic islet beta cells NOS NOS ectopic functional 251.2 Hypoglycemia, unspecified 251.3